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EDITORIAL REVIEW
Neurologists are from Mars. Rheumatologists are from Venus:
differences in approach to classifying the idiopathic
inflammatory myopathies
Lisa Christopher-Stine
Introduction
Men are from Mars, Women are from Venus, the popular book
by John Gray, suggests by its title, that men and women
are as different as beings from other planets. It offers
helpful suggestions for improving men–women relation-
ships by understanding the communication style of the
opposite gender. This metaphor can be applied to neuro-
logists and rheumatologists in the way that we may speak
similar, yet different languages when describing the same
myositis patients. Specifically of interest here are those
with the recently described autoimmune necrotizing
myopathy subtype.
Working in parallel
It has been my experience over the past several years
working in a multidisciplinary clinic with various sub-
specialists – with the exclusive focus of treating patients
with idiopathic inflammatory myopathies (‘myositis’) and
their clinical mimics – that we may, in fact, not always be
practicing synergistically but rather working in parallel.
To what do we owe this communication gap? Why do we
not always speak the same language? As a rheumatologist,
I have ascertained a great deal of knowledge from my
neurology colleagues by observation and discussion
working side by side in the clinical and research settings.
Johns Hopkins University, Baltimore, Maryland, USA
Correspondence to Lisa Christopher-Stine, MD, MPH,
Johns Hopkins Bayview Medical Center, Johns
Hopkins Myositis Center, Mason F. Lord Building
Center Tower, Suite 4100, Baltimore, MD 21224, USA
Tel: +1 410 550 6962; fax: +1 410 550 3542;
e-mail: lcs@jhmi.edu
Current Opinion in Rheumatology 2010,
22:623–626
Purpose of review
Inflammatory myopathy (IIM) classification criteria have been the source of considerable
debate. In the three decades since Bohan and Peter published their criteria which have
long stood as the gold standard for diagnosis in clinical practice as well as inclusion
into clinical trials, more sophisticated understanding of immunopathogenesis, histology,
and specific autoantibody associations has broadened our understanding of these
diseases. This editorial review examines the diverse approaches between different
subspecialists in deriving appropriate IIM classification utilizing this updated knowledge.
Recent findings
Several investigators have proposed improved IIM classification criteria. More recently,
larger scale consensus efforts have been undertaken by various expert groups including
the European Neuromuscular Centre (ENMC) and The International Myositis
Assessment and Clinical Studies Group (IMACS). The intent is to refine the
classification criteria utilizing our enhanced understanding which has matured since the
original publication of Bohan and Peter’s proposal in 1975.
Summary
Many diagnostic/classification criteria have been proposed for different forms of IIM
over the last three decades. The majority of these have been based on clinical
impressions rather than rigorous data analyses or expert consensus and none has been
fully tested for sensitivity or specificity using appropriately powered studies that take
into account relevant disease confounders. Different sets of criteria proposed and
adopted by different specialties hamper the ability to compare clinical studies and
assess clinical trials’ outcomes. Large, multicentered, multispecialty studies are
required to develop improved IIM criteria.
Keywords
autoimmune necrotizing myopathy, Bohan and Peter, myositis, myositis classification
criteria, polymyositis
Curr Opin Rheumatol 22:623–626
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1040-8711
1040-8711 ß 2010 Wolters Kluwer Health | Lippincott Williams & Wilkins DOI:10.1097/BOR.0b013e32833f8f72