Nebulized sildenafil is a selective pulmonary vasodilator in lambs with acute pulmonary hypertension Fumito Ichinose, MD; Juan Erana-Garcia, MD; Jonathan Hromi, BA; Yehuda Raveh, MD; Rosemary Jones, PhD; Lori Krim, PhD; Martin W. H. Clark, BsC; Jeffrey D. Winkler, PhD; Kenneth D. Bloch, MD; Warren M. Zapol, MD P ulmonary artery hypertension is an important feature of acute and chronic lung disease of various etiologies. Systemic vasodilator therapy with intravenous agents is limited by a lack of pulmonary selectivity and can cause both pulmonary and systemic vasodilation with poten- tially catastrophic arterial hypotension. Furthermore, systemic administration of vasodilators may worsen arterial oxygen- ation by increasing blood flow to poorly ventilated lung regions, resulting in in- creased right-to-left intrapulmonary shunting. In contrast to systemically adminis- tered vasodilators, inhaling low concen- trations of nitric oxide (NO) gas has been shown to cause selective pulmonary va- sodilation (1) as the result of rapid inac- tivation of NO by hemoglobin binding on entry into the intravascular space (2). Be- cause the vasodilating effects of NO are largely mediated via cyclic guanosine monophosphate (cGMP) -dependent mechanisms, we hypothesized that inhi- bition of the cGMP-selective phosphodi- esterase type 5 would augment the vaso- dilating effects of inhaled NO by increasing cGMP levels in vascular smooth muscle cells. We reported that an intravenous infusion of zaprinast mark- edly prolonged the pulmonary vasodila- tion induced by inhaled NO (3). Recently, we further demonstrated that enteral ad- ministration of sildenafil, the novel and highly-selective phosphodiesterase type 5 inhibitor that is now clinically available under the trade name of Viagra (Pfizer, New York, NY) (4, 5), caused pulmonary vasodilation in awake lambs with U46619-induced pulmonary hypertension (6). Although aerosolized zaprinast caused selective pulmonary vasodilation and augmented the pulmonary vasodilat- ing effects of inhaled NO (7), intravenous administration of zaprinast caused vaso- dilation of poorly ventilated lung regions and impaired the beneficial effects of in- haled NO on systemic oxygenation in a sheep model of acute lung injury (8). From the Department of Anesthesia and Critical Care (Drs. Ichinose, Erana-Garcia, Raveh, Jones, and Zapol and Mr. Hromi) and the Cardiovascular Research Center and Cardiology Division of the Department of Medicine (Dr. Bloch), Massachusetts General Hospital, Harvard Medical School, Boston, MA; the Department of Chemistry, the University of Pennsylvania (Drs. Winkler and Krim), Philadelphia, PA; and Pfizer Central Research (Mr. Clark), Sandwich, UK. Address requests for reprints to: Fumito Ichinose, MD, Department of Anesthesia and Critical Care, Car- diovascular Research Center, Massachusetts General Hospital, Boston, MA 02114. E-mail: ichinose@ etherdome.mgh.harvard.edu Supported, in part, by National Institutes of Health grant HL42397. Dr. Bloch is an Established Investiga- tor of the American Heart Association. The Massachusetts General Hospital has been granted patents on the inhalation of nitric oxide and phosphodiesterase inhibitors, and the authors have a right to receive royalties. Copyright © 2001 by Lippincott Williams & Wilkins Objective: To determine whether inhalation of aerosolized sil- denafil with and without inhaled nitric oxide (NO) causes selective pulmonary vasodilation in a sheep model of pulmonary hyperten- sion. Design: A controlled laboratory study in instrumented, awake, spontaneously breathing lambs. Setting: Animal research laboratory affiliated with a university hospital. Subject: Twenty Suffolk lambs. Interventions: Lambs were instrumented with a carotid artery catheter, a pulmonary artery catheter, and a tracheostomy tube and studied awake. After baseline measurements, pulmonary hypertension was induced by the continuous infusion of U46619, a thromboxane A 2 analog. After breathing three concentrations of inhaled NO (2, 5, and 20 ppm), lambs were divided into two groups. Group 1 (n 7) breathed aerosols containing 1, 10, and 30 mg of sildenafil alone, and group 2 (n 4) simultaneously breathed NO (2 and 5 ppm) and aerosols containing 10 mg of sildenafil. Hemodynamic measurements were obtained before and at the end of each drug administration. Venous admixture was calculated, and plasma cyclic guanosine monophosphate and sildenafil concentrations were measured. Measurements and Main Results: Aerosols containing 10 mg and 30 mg of sildenafil selectively decreased the pulmonary artery pressure by 21% 3% and 26% 3%, respectively (p < .05 vs. baseline pulmonary hypertension). When 10 mg of silde- nafil was inhaled while simultaneously breathing 2 ppm and 5 ppm NO, the pulmonary artery pressure decreased by 35% 3% and 43% 2% (p < .05 vs. baseline pulmonary hypertension). Inhaled sildenafil did not impair systemic oxygenation, increase right-to-left intrapulmonary shunting, or impair the ability of inhaled NO to reduce right-to-left shunting. Conclusions: Nebulized sildenafil is a selective pulmonary va- sodilator that can potentiate the pulmonary vasodilating effects of inhaled NO. (Crit Care Med 2001; 29:1000 –1005) KEY WORDS: pulmonary hypertension; pulmonary vasodilator; nitric oxide; 3,5-cyclic guanosine monophosphate phosphodies- terase; phosphodiesterase inhibitor; sildenafil; aerosol drug ther- apy; respiratory therapy; inhalation drug administration; sheep 1000 Crit Care Med 2001 Vol. 29, No. 5