AJR:178, April 2002 869
Benign Hepatic Nodules in
Budd-Chiari Syndrome:
Radiologic–Pathologic Correlation with
Emphasis on the Central Scar
OBJECTIVE. The purpose of this study was to determine the imaging features of benign
hepatic nodules in patients with Budd-Chiari syndrome and to correlate them with pathologic
findings, with special attention placed on the presence of a central scar.
MATERIALS AND METHODS. Imaging findings of 59 benign hepatic nodules in four
patients with chronic Budd-Chiari syndrome were analyzed retrospectively, and radiologic–
pathologic correlation was performed in three patients with 50 hepatic nodules who under-
went liver transplantation. All patients underwent multiphasic helical CT. In three patients
with 29 lesions, MR imaging, including a multiphasic dynamic study, was performed. The CT
and MR imaging findings in these patients were compared with those of 103 small hepatocel-
lular carcinomas in 56 other patients (54 of them displayed chronic hepatitis or liver cirrhosis
associated with viral hepatitis but none had Budd-Chiari syndrome). Image analysis was per-
formed by two radiologists with no knowledge of the diagnosis.
RESULTS. All patients with Budd-Chiari syndrome exhibited multiple benign nodules up
to 3 cm in diameter, and 42 of 59 lesions were hypervascular. Microscopically, 15 of 32 nod-
ules demonstrated a central scar; moreover, some nodules closely resembled focal nodular hy-
perplasia. Frequencies of hyperintensity on T1-weighted images (14/29 vs 25/103),
hypointensity on T2-weighted images (7/29 vs 1/103), and the presence of a central scar (6/59
vs 1/103) were significantly higher in benign nodules than in hepatocellular carcinomas ( p <
0.05; Fisher’s exact test). Moreover, for lesions larger than 1 cm, imaging studies revealed a
central scar in six of 15 benign lesions.
CONCLUSION. Benign hepatic nodules in patients with in Budd-Chiari syndrome are
usually small, multiple, and hypervascular. The presence of a central scar is a characteristic
feature in those larger than 1 cm in diameter.
udd-Chiari syndrome is a disorder
resulting from gross outflow block
to hepatic veins with numerous
causes. The liver in patients with Budd-Chiari
syndrome is known to develop severe conges-
tion, fibrosis, and cirrhosis [1]. In association
with Budd-Chiari syndrome, benign regenera-
tive nodules, termed adenomatous hyperplastic
nodules [2], nodular regenerative hyperplasia
[3–5], and regenerative nodules [6–9] have been
described in the literature. On pathologic exam-
ination, benign nodules of greater than 5 mm in
diameter have been observed in 60–80% of pa-
tients with Budd-Chiari syndrome [7, 8]. De-
spite this fact, only a few studies have reported
imaging findings regarding these lesions.
In patients with chronic Budd-Chiari syn-
drome, hepatocellular carcinoma also can
develop [10, 11], and it is important to distin-
guish benign hepatic nodules from hepato-
cellular carcinoma because treatment differs
radically. On radiologic examination, both
benign nodules and hepatocellular carci-
noma have been reported as hypervascular
[6]. On the other hand, benign nodules com-
posed of fairly normal hepatocytes often
have a central scar and resemble focal nodu-
lar hyperplasia pathologically [7–9]. There-
fore, the presence of a central scar may
suggest benignity. However, to our knowl-
edge, no radiologic study has documented
the presence of a central scar of benign le-
sions in Budd-Chiari syndrome. In addition,
the incidence of central scars in hepatocellu-
lar carcinoma remains unclear. The purpose
of our investigation was to describe the im-
aging appearance of benign hepatic nodules
in Budd-Chiari syndrome and to compare it
Yoji Maetani
1
Kyo Itoh
2
Hiroto Egawa
3
Hironori Haga
4
Takaki Sakurai
5
Naoshi Nishida
6
Fumie Ametani
1
Toshiya Shibata
2
Takeshi Kubo
1
Koichi Tanaka
3
Junji Konishi
1
1
Department of Radiology, Kyoto University Graduate
School of Medicine, 54 Kawahara-cho, Shogoin, Sakyo-ku,
Kyoto, Japan, 606-8507. Address correspondence to
Y. Maetani.
2
Department of Radiology, Kyoto University Hospital,
Kyoto, Japan, 606-8507.
3
Department of Transplantation Immunology and
Transplant Surgery, Kyoto University Graduate School of
Medicine, Kyoto, Japan, 606-8507.
4
Organ Transplantation Unit, Kyoto University Hospital,
Kyoto, Japan, 606-8507.
5
Laboratory of Pathology, Kyoto Katsura Hospital,
17 Yamada Hirao-cho, Nishikyo-ku, Kyoto, Japan.
6
Department of Medicine and Clinical Science, Kyoto
University Hospital, Kyoto, Japan, 606-8507.
AJR 2002;178:869–875
0361–803X/02/1784–869
© American Roentgen Ray Society
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