Introduction Meningioangiomatosis (MA) is a rare, benign hamart- omatous lesion of cerebral cortex and leptomeninges [1]. Pathologically, it is characterised by cortical meningo- vascular proliferation and leptomeningeal calcifications [2]. The common clinical symptoms are headache and seizure. Although the aetiology and pathogenesis are unknown, neurofibromatosis is associated in half of the patients with MA. We report the imaging and patho- logic findings of two cases of MA. Case reports Case 1 An 8-year-old boy had a 7-year history of recurrent, simple partial seizures. During a seizure he had clonic movement predominantly in the right upper extremity. The EEG showed rhythmic spikes in the left temporo-parietal lobe and both frontal lobes. MRI revealed a3·2·4-cm, ill-defined subcortical mass in the left frontal lobe that had a broad base on the adjacent dura. The signal intensity of the tumour was isointense with the cortex on T1-weighted (T1-W) and T2 weighted (T2-W) images. On contrast-enhanced images, the tumour was better defined with mild enhancement, and the attached dura enhanced moderately (Fig. 1). Dark signal spots suggestive of calcifications were identified within the mass on all sequences. The mass was diffusely decreased in signal intensity on the gradient-echo image, suggesting associated haemorrhage within the tumour (Fig. 1d). During surgery, the tumour was found in the left precentral gyrus as an ovoid cortical mass with firm consistency. It was easily demarcated from the surrounding normal tissue and there was no invasion of the overlying dura. Microscopic examination (Fig. 1e) revealed leptomeningeal and vascular proliferations and some psammomatous calcifications within the mass, which was compatible with meningioangiomato- sis. Some foci of haemorrhage were revealed in the tumour. The patient has remained free of seizures since surgery. Case 2 A 3-year-old boy complained of headache and suffered a seizure 3 days after minor head trauma. CT (Fig. 2a) showed extensive ORIGINAL ARTICLE Pediatr Radiol (2002) 32: 96–98 DOI 10.1007/s00247-001-0601-7 Wha-Young Kim In-One Kim Woo Sun Kim Jung-Eun Cheon Kyung Mo Yeon Meningioangiomatosis: MR imaging and pathological correlation in two cases Received: 30 March 2000 Revised: 5 March 2001 Accepted: 23 August 2001 Published online: 11 December 2001 Ó Springer-Verlag 2001 W.-Y. Kim ® I.-O. Kim (&) ® W.S. Kim J.-E. Cheon ® K.M. Yeon Department of Radiology and Institute of Radiation Medicine, Neuroscience Research Institute, Seoul National University Medical Research Centre, Seoul, South Korea Tel.: +82-2-7603608 Fax: +82-2-7475781 I.-O. Kim Department of Radiology, Seoul National University Children’s Hospital, 28 Yongon-dong, Chongno-gu, Seoul 110-744, South Korea Abstract Meningioangiomatosis is a rare, benign neoplastic disorder in- volving the cortex and leptomenin- ges. The pathological findings are characterised by proliferation of meningothelial cells and leptomen- ingeal vessels and calcifications within the mass. We experienced two cases of pathologically confirmed meningioangiomatosis, one as a solitary cortical mass with calcifica- tion and the other as a cortical lesion manifested as extensive intracranial haemorrhage. On MRI, the first case showed an isointense cortical mass in the left frontal lobe and homo- geneous enhancement on the contrast-enhanced study. The sec- ond case showed a target-like lesion with a peripheral dark signal rim on T2-weighted images accompanied by extensive haemorrhage in the adjacent frontal lobe and lateral ventricles. Keywords Meningioangiomatosis ® MR imaging ® Pathological correlation