birth, proliferate in the first months of life and then gradually involute throughout childhood. Congenital hemangiomas are further subclassified into rapidly involuting (RICH) and non-involuting (NICH) congenital hemangioma. Recently, a new variant of RICH showing fetal involution has been described. The prominent part of the life cycle of this variant of RICH (ie, proliferation and rapid involution) seems to start prenatally, whereas regression in typical RICH usually occurs in early infancy.Our case seems to confrm the existence of such variant of RICH. Key words: Congenital hemangioma; Pediatric dermatology; Perina- tology; Neonatology © 2019 The Author(s). Published by ACT Publishing Group Ltd. All rights reserved. Silecchia V, Valerio E, Filippone M, Balao L, Cherubin E, Rigon L, Grimalt R, Cutrone M. Phakomatosis Pigmentovascularis Cesioflammea. Journal of Dermatological Research 2019; 4(2): 189-190 Available from: URL: http//www.ghrnet.org/index.php/jdr/ article/view/2736 Abbreviations RICH: rapidly involuting congenital hemangioma; NICH: non- involuting congenital hemangioma PATIENT PRESENTATION A term newborn from a normal pregnancy came to our attention at 1 month of life for the presence of an atrophic lesion in the nucal region, clinically resembling an involuting hemangioma (Figure 1). This hypothesis was also strengthened by dermoscopy, which showed some residual ectasic capillaries (Figure 1, box). The mother reported to have noticed posteriorly at the base of the neck, soon after birth, the presence of an ovalar area of atrophic skin lifted in folds. No cutaneous markers suggestive of disraphism (ie, pits, fur, lipomas) were present. Therefore, our working diagnosis was that of an in utero rapidly involuting congenital hemangioma (RICH). Given the absence of associated symptoms, we decided not to perform biopsy and opted for clinical follow up. 1 Department of Woman and Child Health, University of Padua, Padova, Italy; 2 Neonatal Intensive Care Unit, “Pietro Cosma” Hospital, Camposampiero (Padova), Italy; 3 Pediatric Dermatology Unit, “Dell’Angelo” Hospital, Mestre (Venezia), Italy; 4 Universitat Internacional de Catalunya. Dermatology, Sant Cugat del Vallès. Barcelona, Spain. Confict-of-interest statement: The author(s) declare(s) that there is no confict of interest regarding the publication of this paper. Open-Access: This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Com- mons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non- commercially, and license their derivative works on diferent terms, provided the original work is properly cited and the use is non- commercial. See: http://creativecommons.org/licenses/by-nc/4.0/ Correspondence to: Enrico Valerio, Pediatric Intensive Care Unit, Ospedale San Bortolo, Vicenza, Italy. Email: enrico.valerio.md@gmail.com Telephone: +39 0444 75 2887 Fax: +39 0444 75 2796 Received: July 30, 2019 Revised: August 6, 2019 Accepted: September 1, 2019 Published online: December 19, 2019 ABSTRACT A term newborn was evaluated for the presence of a lesion resembling an involuting hemangioma; dermoscopy showed some residual ectasic capillaries, consistent with the diagnosis. At 5 months, lesion appeared in further light regression, comparable to that of a classical capillary hemangioma at 2 years of life. Pediatric hemangiomas are classified into infantile and congenital hemangioma. Infantile hemangiomas typically are very pale at TOPIC HIGHLIGHT RICH (Rapidly Involuting Congenital Hemangioma) with Fetal Involution Valeria Silecchia 1 , Silvia Palatron 2 , Enrico Valerio 2 , Francesca Favot 3 , Ilaria Mattei 3 , Ramon Grimalt 4 , Mario Cu- trone 3 189 J. of Dermatological Res. 2019 December; 4(2): 189-190 ISSN 2413-8223 Online Submissions: http://www.ghrnet.org/index./jdr/ doi:10.17554/j.issn.2413-8223.2019.04.46-10 Journal of Respiratory Research