https://doi.org/10.1177/0004867417744256
Australian & New Zealand Journal of Psychiatry, 00(0)
Australian & New Zealand Journal of Psychiatry
1
© The Royal Australian and
New Zealand College of Psychiatrists 2017
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Primary genetic dystonia
and first episode of
psychosis
Tamoor Mirza
1
and
Muhammad Hassan
Majeed
2
1
headspace Youth Early Psychosis Program,
headspace Darwin, Casuarina, NT, Australia
2
Natchaug Hospital, Mansfield Center, CT,
USA
Corresponding author:
Tamoor Mirza, headspace Youth Early
Psychosis Program, headspace Darwin,
Casuarina, NT 0810, Australia.
Email: tmirza@anglicare-nt.org.au
DOI: 10.1177/0004867417744256
To the Editor
The association of spontaneous dyski-
netic movement disorders and psy-
chosis in anti-psychotic naïve patients
has been established (Pappa and
Dazzan, 2009). In a high-risk popula-
tion, baseline dyskinesia warrants
thorough evaluation for psychosis
(Callaway et al., 2014). We present a
case of an adolescent with primary
genetic dystonia (PGD) who devel-
oped an early-onset first episode of
psychosis (FEP).
At 10 years of age, B was diagnosed
with a PGD with superior intellect. She
initially presented with facial dystonia,
dysarthria, difficulty with handwriting,
gait problems and bradykinesia. Genetic
testing revealed 1.1 Mb duplication at
chromosome 8p23.2 to 8p23.3. She
was prescribed dopaminergic drugs for
the movement disorder with no signifi-
cant clinical improvement. At the age
of 14 years, she exhibited negative
symptoms of a prodromal psychotic ill-
ness followed by distressing auditory
hallucinations and persecutory delu-
sions. Movement disorder was the only
identifiable risk factor for psychosis.
She was treated with low-dose olan-
zapine and positive symptoms resolved
in 4 weeks. The primary movement
disorder symptoms were unaffected
with olanzapine as evident by stable
scores of 4 on Abnormal Involuntary
Movement Scale.
PGD, which presents with dyski-
nesia, can be an independent risk fac-
tor for the development of FEP.
These dyskinetic movements are bio-
logical predictor of pathogenesis
intrinsic to psychosis. In the popula-
tion with baseline movement disor-
ders, the prevalence of psychosis is
up to 20% (Callaway et al., 2014).
Patients with PGD present with
movement abnormalities hence are
at high risk for the development of
psychosis.
It is clinically pertinent to fre-
quently screen patients with PGD for
prodrome and symptoms of psycho-
sis. Close clinical observation and cog-
nitive behavioral therapy in suspected
cases are advised. Longer duration of
untreated psychosis are associated
with worse clinical, functional and
cognitive outcomes in FEP (Díaz-
Caneja et al., 2015).
For the treatment of psychosis, it
is prudent to consider lower doses
of anti-psychotic medications with
favorable extra pyramidal symptoms
(EPS) side effects. The ratio of affin-
ity for D
2
and 5-HT
2A
receptors
determines the EPS liability of these
medications. EPS side effects could
be hard to distinguish from primary
dystonia itself.
Clinicians should periodically
screen PGD patients for prodromal
symptoms and psychosis and if appro-
priate refer to the specialized care.
Larger scale studies controlling for
confounding factors are necessary to
establish a correlation of PGD and
psychosis.
Declaration of Conflicting
Interests
The author(s) declared no potential con-
flicts of interest with respect to the
research, authorship and/or publication of
this article.
Funding
The author(s) received no financial sup-
port for the research, authorship and/or
publication of this article.
References
Callaway DA, Perkins DO, Woods SW, et al.
(2014) Movement abnormalities predict tran-
sitioning to psychosis in individuals at clinical
high risk for psychosis. Schizophrenia Research
159: 263–266.
Díaz-Caneja CM, Pina-Camacho L, Rodríguez-
Quiroga A, et al. (2015) Predictors of out-
come in early-onset psychosis: a systematic
review. Npj Schizophrenia. Epub ahead of print
4 March. DOI: 10.1038/npjschz.2014.5.
Pappa S and Dazzan P (2009) Spontaneous move-
ment disorders in antipsychotic-naive patients
with first-episode psychoses: A systematic
review. Psychological Medicine 39: 1065–1076.
Letter
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