1 BACKGROUND General Head and neck cancers are the sixth most common cancers among males and twice in prevalence when compared with females. 1 Head and neck cancers are composed of cancers arising from the paranasal sinuses, nasopharynx, oral cavity, oropharynx, hypopharynx, and larynx. 2 The cancers arising from the salivary glands and lip are not reviewed in this chapter. The following are the main risk factors 3–5 : Tobacco and alcohol use. Infection with human papillomavirus (HPV), particularly HPV-16 infection, is one of the main causes of oropharyngeal cancers. No screening test is available for head and neck can- cers. 6 The hypopharyngeal, laryngeal, oropharyngeal, and nasopharyngeal cancers present with distant metasta- ses in 19%, 16%, 13%, and 10% of cases, respectively. 7 Cervical lymph node metastasis is the presenting sign in about 2% to 9% of patients with head and neck squamous cell carcinoma (HNSCC) with an unknown primary site of cancer. 8 Early Clinical Symptoms 9 Cervical lymphadenopathy Long-lasting oral cavity ulcer or sore throat Dysphagia Hoarseness Nasal airway obstruction Standard Diagnostic Procedures 10 Clinical examination Panendoscopy and biopsy Fine-needle aspiration or core biopsy CT, MRI, and PET/CT (if indicated) HPV diagnostics Standard Treatment 11–13 Surgery Radiation therapy Chemotherapy Targeted therapy Prognostic Factors 13–15 Tumor location (worse in hypopharyngeal cancers) Tumor size (worse if larger) Lymph node status (worse if contralateral neck nodes are involved) Histologic grade (worse if high grade/poorly differ- entiated) Overexpression of epidermal growth factor receptor (worse prognosis) Tumors not associated with HPV (worse prognosis) Five-Year Survival 16 Stage I: 77% Stage II: 61% Stage III: 57% Stage IV: 42% TUMOR CHARACTERISTICS AND TYPICAL BEHAVIOR Histopathology 2,17 Squamous cell carcinoma: >90% Others (adenocarcinoma, esthesioneuroblasto- ma, lymphoepithelioma, adenoid cystic cancer): <10% Distribution and Localization T-primary 2,18 Paranasal sinuses Nasopharynx Oral cavity Oropharynx Hypopharynx Larynx N-lymph nodes 2 The primary localization of the lymph nodes and their cervical level are provided in Table 1.1. CHAPTER 1 Head and Neck Cancers MOHSEN BEHESHTI • RATHAN M. SUBRAMANIAM • ALIREZA REZAEE • MARTIN BURIAN • WERNER LANGSTEGER