Biochimica et Biophysica Acta, 942 (1988) 45-56 45
Elsevier
BBA 74035
The new basement membrane antigen recognized by the monoclonal antibody
GB3 is a large size glycoprotein: modulation of its expression by retinoic acid
Patrick Verrando, Anne Pisani and Jean-Paul Ortonne
Laboratoire de Recherches Dermatologiques, UER M$decine, Nice (France)
(Received 25 November 1987)
(Revised manuscript received 6 April 1988)
Key words: Basement membrane; Antigen; Glycoprotein; Monoclonal antibody; Retinoic acid; (Human epidermis)
Further biochemical investigations on the hemidesmosome-associated epidermal basement membrane com-
ponent recognized by the monoclonal antibody GB3 are presented in this study. We previously found that
the expression of this constituent is impaired in a severe genodermatosis termed lethal junctional epidermol-
ysis bullosa. We demonstrate now that this factor is a very large glycoprotein (apparent molecular weight,
600 kDa) made up of polypeptides in the range of 93.5 to 150 kDa, and containing N-linked oligosaccharide
chains. Both endo-fl-N-acetylglucosaminidases and neuraminidase hydrolysis, as well as concanavalin A
binding experiments were performed on the GB3 radioimmunoprecipitated polypeptides from cultured
human keratinocytes. They showed that the antigen subunits probably bear both 'high-mannose' and
'complex' type glycosidic chains. The chronic exposure of cultured human keratinocytes to retinoic acid
(10 -s to 10-6 M) resulted in no apparent changes in the overall bulk of these glycosidic chains, but a
dose-dependent increase of synthesis and secretion of the antigen was observed. A relative induction factor
of 4 was obtained in cultures treated with 10 -6 M retinoic acid. This induction was also observed
morphologically by indirect immunofluorescence at the basement membrane zone from cultured human
keratinocytes grown on dead de-epidermized dermis. These results further emphasize the influence of
glycoproteins in cell-cell and cell-substratum attachment. Furthermore, the ability to modulate this antigen
may be relevant for the understanding of the molecular defect involved in lethal junctional epidermolysis
bullosa.
Introduction
Basement membranes are specialized extracell-
ular matrices which, by forming a complex scaf-
fold, are involved in various biological processes
such as spreading, migration, attachment and dif-
ferentiation of their overlying cell population [1,2].
Although the total number of components re-
Correspondence: J.-P. Ortonne, Laboratoire de Recherches
Dermatologiques, UER Mrdecine, avenue de Valombrose,
06034 Nice Cedex, France.
quired to form a functional basement membrane
is still unknown, some biochemical constituents
have been characterized and ultrastructurally
localized in mammalian basement membranes,
specially in the human epidermal basement mem-
brane [2,3]. A comprehensive characterization of
the ubiquitous basement membrane proteins and
their poorly understood relationships is sought,
since the basement membrane is implicated in a
variety of diseases, such as diabetes mellitus and
polycystic kidney disease, and skin disorders such
as epidermolysis bullosa acquisita [2].
0005-2736/88/$03.50 © 1988 Elsevier Science Publishers B.V. (Biomedical Division)