https://doi.org/10.1177/1352458519891984
https://doi.org/10.1177/1352458519891984
MULTIPLE
SCLEROSIS MSJ
JOURNAL
journals.sagepub.com/home/msj 1
Multiple Sclerosis Journal
1–10
DOI: 10.1177/
1352458519891984
© The Author(s), 2019.
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Introduction/background
Multiple sclerosis (MS) is a chronic and progressive
central nervous system (CNS) disorder characterized
by demyelination, immune-mediated inflammation,
and neurodegeneration. Pediatric-onset multiple scle-
rosis (POMS) occurs in approximately 3% of MS cases
and is considered a rare disorder of childhood.
1
As
such, less is known about this MS subgroup and how
the disease may affect ongoing neurodevelopment.
Cognitive impairment occurs in up to 65% of all adults
with MS
2
and is estimated to occur in approximately
one-third of POMS cases.
3–7
The long-term conse-
quences for these children remain unclear; however,
adults with pediatric- relative to adult-onset MS have
worse cognitive performance.
8,9
Routine cognitive
screening is now recommended for all MS patients
10
and is particularly important for those in the pediatric
age group with MS as they could be at greatest risk of
cognitive involvement and related complications.
Cognitive screening early in the disease course is
important since the identification of problems and
prompt intervention could hopefully lead to better
Cognitive processing speed in pediatric-onset
multiple sclerosis: Baseline characteristics of
impairment and prediction of decline
Asya I Wallach , Michael Waltz, T Charles Casper, Gregory Aaen, Anita Belman,
Leslie Benson, Tanuja Chitnis , Mark Gorman, Jennifer Graves , Yolanda Harris,
Timothy E Lotze, Soe Mar, Manikum Moodley, Jayne M Ness, Mary Rensel, Moses Rodriguez,
John W Rose, Teri Schreiner, Jan-Mendelt Tillema, Emmanuelle Waubant,
Bianca Weinstock-Guttman, Leigh E Charvet and Lauren B Krupp;
on behalf of the US Network of Pediatric Multiple Sclerosis Centers
Abstract
Background: Cognitive impairment occurs in approximately one-third of pediatric-onset multiple scle-
rosis (POMS) patients. The Symbol Digit Modalities Test (SDMT), a widely used cognitive screen in
adults, has yet to be incorporated early into the standard care of POMS.
Objective: To screen for cognitive impairment early in the course of POMS and analyze predictive fac-
tors.
Methods: Of the 955 POMS or clinically isolated syndrome (CIS) patients prospectively assessed from
March 2014 to July 2018, 500 POMS and 116 CIS patients met inclusion criteria (disease onset before
the age of 18, one or more SDMTs, and 8 years or older at the time of testing). Those with relapse were
analyzed separately from those who were relapse-free.
Results: At initial assessment, the mean (interquartile range (IQR)) age at symptom onset was 13.5 years
(12.0, 15.9) and the mean (±SD) disease duration was 3.0 ± 2.9 years. Impaired processing speed occurred
in 23.4% of POMS and in 16.4% of CIS. On serial testing (n = 383, mean follow-up: 1.8 years), 14.1% had
clinically meaningful decline predicted by older age of multiple sclerosis (MS) onset and male gender.
Disease relapse or steroid use led to transient worsening on the SDMT.
Conclusion: Early in the disease, some POMS and CIS patients are at risk for cognitive impairment and
subsequent decline.
Keywords: Pediatric-onset multiple sclerosis, pediatric MS, symbol digit modalities test, cognition,
cognitive processing speed, multiple sclerosis
Date received: 16 July 2019; revised: 7 October 2019; accepted: 23 October 2019.
Correspondence to:
LB Krupp
Pediatric Multiple Sclerosis
Center, Department of
Neurology, NYU Langone
Medical Center, 222 East
41st Street, 10th Floor, New
York, NY 10017, USA.
Lauren.Krupp@
nyulangone.org;
Twitter: @AsenkaMD
Asya I Wallach
Anita Belman
Leigh E Charvet
Lauren B Krupp
Pediatric Multiple Sclerosis
Center, Department of
Neurology, NYU Langone
Medical Center, New York,
NY, USA
Michael Waltz
T Charles Casper
John W Rose
Pediatrics, The University
of Utah, Salt Lake City,
UT, USA
Gregory Aaen
Pediatric Multiple Sclerosis
Center, Loma Linda
University, Loma Linda,
CA, USA
Leslie Benson
Tanuja Chitnis
Partners Multiple Sclerosis
Center, Massachusetts
General Hospital, Harvard
Medical School, Boston,
MA, USA
Mark Gorman
Boston Children’s Hospital,
Boston, MA, USA
Jennifer Graves
Pediatric MS Center,
Neurology, University of
California, San Diego, San
Diego, CA, USA
Yolanda Harris
Jayne M Ness
Center for Pediatric-Onset
Demyelinating Disease,
Children’s of Alabama,
University of Alabama at
Birmingham, Birmingham,
891984MSJ 0 0 10.1177/1352458519891984Multiple Sclerosis JournalAI Wallach, M Waltz
research-article2019 2019
Original Research Paper