Biclonal Chromosome Evolution of Chronic
Myelomonocytic Leukemia in a Child
Liliane Massaad, Marguerite Prieur, Claude Leonard,
and Bernard Dutrillaux
ABSTRACT: A monosomy 7 was first detected in a 6-month-old boy with a chronic myelomonocytic
leukemia. After etoposide treatment, relapse occurred after 29 months, with transformation
of the disease into an acute myeloblastic leukemia. After bone marrow transplanta-
tions, two abnormal clones were found in marrow cells: 45,XY,-7,del(12)(pl lp12)(66%), and
45,XY,-7,t(3;12)(q26;p12)(33%). Several karyotypic studies performed until the terminal
phase exhibited the persistence of these two clones in the same proportion, although both
independently acquired additional and often similar anomalies. The clone with t(3;12)
acquired der(7),der(11),der(17),der(8),der(lO),-5,-20, and the clone with del(12p),
del(5q),der(4),der(8),der(10),der(17),-5,-20. The anomalies in 12p12 appear to represent an
important although secondary event of the neoplastic process. The other anomalies may corre-
spond to either those of a secondary acute nanlymphocytic leukemia, since they occurred after
treatment by etoposide and alkylating agents, or to the natural evolution of myelomonocytic
leukemia.
INTRODUCTION
Chronic myelomonocytic leukemia (CMMoL) and/or myelodysplastic syndromes
(MDS) of childhood are principally characterized by monosomy 7 [1, 2]. Although
this anomaly has been known for some time, little is known about secondary chro-
mosomal changes associated with -7. Recently, a rearrangement involving chromo-
some 11 was described in two children [3]. We report a case of CMMoL in a child in
whom monosomy 7 was first detected. After bone marrow transplantation, further
rearrangements occurred and two independent clones were observed until the termi-
nal phase of the disease. This unusual chromosome evolution is described.
CASE REPORT
The diagnosis of a hematological disorder was first suspected in a 6-month-old boy.
Fever, pallor, and hypotrophy were associated with hepatosplenomegaly, multiple
enlarged lymph nodes, and hematodermy. Blood and bone marrow cell counts were
characteristic of a chronic myelomonocytic leukemia (Table 1). A treatment with
etoposide at age 9, 10, and 11 months stabilized the disease, and no signs of transfor-
mation were noticed until age 29 months. At this age, transformation of the disease
From the BiologySection (L. M., M. P., B. D.), Institut Curie and Laboratoired'HistologieEmbryologie
Cytog6n~tique(C. L.), C.H. BicStre, BicStre,France.
Address reprint requests to: Dr. Marguerite Prieur, Institut Curie, Section de Biologie, URA
620, C.N.R.S. 26, rue d'Ulm, 75231 Paris, Cedex 05, France.
Received March 29, 1989; accepted June 30, 1989.
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© 1990 Elsevier Science PublishingCo., Inc. Cancer Genet Cytogenet44:131-137 (1990)
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