Open Journal of Anesthesiology, 2018, 8, 172-182 http://www.scirp.org/journal/ojanes ISSN Online: 2164-5558 ISSN Print: 2164-5531 DOI: 10.4236/ojanes.2018.85018 May 31, 2018 172 Open Journal of Anesthesiology Anesthetic Management for Quadricuspid Aortic Valve Repair: Case Report and Literature Review Lúcia Caroline Schons Correa 1 , Érica Mendonça Reiff Carlos 1 , Paula Cristina Leitão de Assunção 1 , José Eduardo Guimaraes Pereira 2 , Carlos Darcy Alves Bersot 1 1 Department of Anesthesiology, Medical Sciences College at Hospital Universitário Pedro Ernesto (HUPE), Universidade do Estado do Rio de Janeiro (UERJ), Rio de Janeiro, Brazil 2 Department of Anaesthesiology, Botucatu Medical School, Universidade Estadual Paulista, São Paulo, Botucatu, Brazil Abstract Quadricuspid aortic valve (QAV) is a rare congenital cardiac anomaly with prevalence less than 0.01% in autopsy series. It can be found as an isolated anomaly, and the patient may be asymptomatic, but is often associated with aortic insufficiency in 68% of the cases. Transthoracic echocardiography (TTE) and transesophageal echocardiography (TEE) are currently used as a diagnostic and follow-up method for this anomaly. The objective of the present paper is through the clinical case report of a 60 year old patient sub- mitted to surgical correction of QAV, to relate some clinical aspects of the disease and to discuss the anesthetic management for this group of patients, in addition, emphasizing the importance and the increasing use of the TEE in the intraoperative period in cardiac surgeries. Keywords Quadricuspid Aortic Valve, Anesthetic Management, Transesophageal Echocardiography 1. Introduction There are two classification systems for QAV: The Hurwitz & Roberts [1], in which the QAV is classified according to the size of the supranumerary cusp into seven categories from A to G, and to which Vali [2] has added the H type (Fig- ure 1). And the system proposed by Nakamura et al. [3], in which the classifica- tion is based on the position of the supranumerary cusp, whether it is located How to cite this paper: Correa, L.C.S., Carlos, É.M.R., de Assunção, P.C.L., Perei- ra, J.E.G. and Bersot, C.D.A. (2018) Anes- thetic Management for Quadricuspid Aor- tic Valve Repair: Case Report and Litera- ture Review. Open Journal of Anesthesiol- ogy, 8, 172-182. https://doi.org/10.4236/ojanes.2018.85018 Received: March 8, 2018 Accepted: May 28, 2108 Published: May 31, 2108 Copyright © 2018 by authors and Scientific Research Publishing Inc. This work is licensed under the Creative Commons Attribution International License (CC BY 4.0). http://creativecommons.org/licenses/by/4.0/ Open Access