1 3 Int Urol Nephrol (2016) 48:1771–1775 DOI 10.1007/s11255-016-1365-1 UROLOGY - REVIEW Congenital lymphovascular malformations with urological symptoms: a report of two cases and review of the literature Miklos Romics 1 · Geza Tasnadi 2 · Balint Sulya 3 · Andras Kiss 3 · Miklos Merksz 3 · Peter Nyirady 1 Received: 2 March 2016 / Accepted: 30 June 2016 / Published online: 15 July 2016 © Springer Science+Business Media Dordrecht 2016 therapeutical success is graded by Browse’s scoring system. According to that, our choices of management achieved the best possible outcome in both cases below. Conclusions Although conservative ways of therapy are known and widely used, in more advanced cases surgi- cal help is often needed to reach long-term improvement. In situations where significant mass of chyle has accu- mulated causing severe complaints, conservative therapy should not to be started. Surgical solutions provide fast and lasting improvement for patients suffering from congenital lymphovascular malformations. Keywords Lymphoedema · Lymphovascular · Malformations · Management Introduction Congenital lymphovascular malformations and lymph cir- culatory disorders may be the rarest (only 2:1000 in the 3-year age group) and most complicated areas of vascu- lar surgery and—through their symptoms—urology [1]. Obstructions in the abdominal lymphoid system can be present since childbirth, and symptoms usually occur in the early years. However, it is possible that the disorder stays latent till adulthood. Clinical manifestations are highly diverse: The vis- ible symptoms can be different as the incompetent lym- phovenous sections vary. First, these blocked lymph veins get dilated and the deformed venous valves will cease to prevent reverse lymph flow. The slowed lym- phoid circulation will lead to the vein’s disruption and lymph edema. After the lymph steps out of the circula- tory system, it will penetrate into the peritoneum, bow- els, thorax, scrotum, labia or the lower extremities and Abstract Objectives To collect and review the diagnostic and thera- peutic solutions for primary and congenital lymphovascular malformations leading to urological symptoms in child- hood and also to find the most efficient therapeutic algo- rithms managing such conditions. Methods In our work, we assemble all the diagnostic and therapeutic tools for lymphovascular malformations with urological–urogenital symptoms and demonstrate the inter- ventional therapeutic algorithms through two of our cases where surgery (laparoscopic intervention and clipping of the lymph vessel) had to be performed to stop lymphoid leakage and restore anatomy. Results In cases, where lymphovascular malformations and urological–urogenital symptoms are both present, * Miklos Romics miklos_romics@gmx.com Geza Tasnadi meditas.bt@chello.hu Balint Sulya bsulya@gmail.com Andras Kiss kissandras@heimpalkorhaz.hu Miklos Merksz merksz@heimpalkorhaz.hu Peter Nyirady nyirady.peter@med.semmelweis-univ.hu 1 Department of Urology and Urooncology, Semmelweis University, Ulloi Str 78/b, Budapest 1082, Hungary 2 Department of Surgery, Heim Pál Children’s Hospital, Budapest, Hungary 3 Department of Urological Surgery, Heim Pál Children’s Hospital, Budapest, Hungary