Available online www.jocpr.com Journal of Chemical and Pharmaceutical Research, 2014, 6(8):312-314 Research Article ISSN : 0975-7384 CODEN(USA) : JCPRC5 312 Childhood pityriasis rubra pilaris-A case report Ajay Kumar Jena 1 , Mrutunjay Dash 2 , Maitreyee Panda 1 and Nibedita Patro 1* 1 Department of Skin & VD, IMS & SUM Hospital, S‘O’A University, Bhubaneswar, Odisha, India 2 Department of Paediatrics, IMS & SUM Hospital, S‘O’A University, Bhubaneswar, Odisha, India _____________________________________________________________________________________________ ABSTRACT Pityriasis rubra pilaris, a follicular hyperkeratotic disease affecting the skin can manifest in the young as well as elderly. The etiology is unknown and has a self remitting course in most of the cases. Recently an HIV associated type has been added to the classification because of its unique clinical features. Reporting of childhood pityriasis rubra pilaris is important to highlight the clinical features to the general physician. Key words: Pityriasis rubra pilaris, papulosquamous dermatosis, follicular hyperkeratosis _____________________________________________________________________________________________ INTRODUCTION Pityriasis rubra pilaris (PRP) is an idiopathic papulosquamous keratotic dermatosis. It affects men and women equally with two peaks of age of onset in first and fifth to sixth decades. [1, 2] Six types of PRP have been described. Griffiths [3] divided PRP into 5 categories: type I - classic adult type, type II - atypical adult type, type III - classic juvenile type, type IV - circumscribed juvenile type, and type V - atypical juvenile type. More recently, an HIV-associated type [4] (type VI) has been added to this classification system which has same manifestation as type I along with acne conglobata, hidradenitis suppurativa and lichen spinulosus. Because of the rare reporting of the disease in childhood, we are reporting this classical case of childhood onset PRP. EXPERIMENTAL SECTION A fourteen years old girl presented with complaints of scaly papular rash over whole body since two months. The disease started as thickening and scaling over palms and soles 1 year back. Gradually she developed horny papular lesions over elbows and knees extending to trunk and extremities. On examination she had diffuse involvement of the skin (Figure 1 and 2) with follicular keratotic papules, coalescing to form scaly plaques over elbows, knees and back and areas of sparing in between. Bilateral palms (Figure 3) and soles were thickened and rough to touch.