165 www.pediatriadanas.com
We report a case of a 16-year-old girl with hyaline-vascular type
of abdominal Castleman’s disease. The patient presented with a
history of palpable mass below left ribcage for 6 months. On
admission the girl was in good general condition. Physical exami-
nation showed a palpable mass in the left hemiabdomen but was
otherwise unremarkable. Laboratory fndings were within normal
limits except hypergammaglobulinemia with elevated immuno-
globulin A level. Computed tomography (CT) revealed well-de-
marcated homogeneous mass, extending from left diaphragm to
the lower pole of left kidney, as well as from peritoneum to the
pancreas. CT-guided biopsy was performed. A biopsy material
was considered insuffcient for defnitive diagnosis. A complete
surgical resection was done, and a diagnosis of hyaline-vascu-
lar type of Castleman’s disease was established. Eight years af-
ter surgery the patient is in complete remission. Conclusion -
Castleman’s disease is a rare benign lymphoproliferative disor-
der, whose early recognition can be diffcult due to nonspecifc
symptoms and radiologic fndings. The right pathohistological
diagnosis and appropriate staging of the disease are crucial in the
treatment planning.
Key words: Castleman’s disease ▪ Lymphoproliferative disorder
▪ Child
Introduction
Castleman’s disease (CD) is a benign lymphoproliferative
disorder, with unknown aetiology. There are localized or
unicentric and systemic or multicentric forms. CD most
often presents as a solitary soft tissue mass in the media-
stinum, and may be located extra-thoratically: in the neck,
Case report
Jelena ROGANOVIĆ
1
, Petra ĆOZA
1
, Nives JONJIĆ
2
CASTLEMAN’S DISEASE – CASE REPORT
1
Department of Pediatrics
Clinical Hospital Center Rieka
Republic of Croatia,
2
Department of Pathology
School of Medicine
University of Rieka
Republic of Croatia
Jelena Roganović
Department of Pediatrics
Clinical Hospital Center Rieka
Istarska 43
HR - 51000 Rieka
Republic of Croatia
jelena.roganovic1@ri.t-com.hr
Tel.: + 385 51 659 103/109
Fax.: + 385 51 623 126
Received: August 8, 2012
Accepted: September 22, 2012
Copyright © 2012 by University
Clinical Center Tuzla.
E-mail for permission to publish:
paediatricstoday@ukctuzla.ba
Paediatrics Today 2012;8(2):165-171
DOI 10.5457/p2005-114.53