83 Spring 2023. Volume 11. Number 2 Shanjida Sharmim 1* , Syed Saimul Huque 1 , Golam Muin Uddin 1 , Afroza Begum 1 , Romana Akbar 1 , Delwar Hossain 1 1. Department of Pediatric Nephrology, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.41961 Case Report Glomerulocystic Kidney Disease and End-stage Renal Disease in a Child: A Rare Case Report and Literature Review Glomerulocystic kidney disease (GCKD) is characterized by cystic dilatation of the Bowman’s capsule and adjacent tubules. It is a rare form of cystic kidney disease and can occur at any age. Sometimes GCKD may not be differentiated from other cystic kidney diseases. It usually presents with renal failure. Here, we reported a case of a four-year-old girl presented with end-stage renal disease who had glomerulocystic kidney disease in renal histopathology. Keywords: Renal cyst, Glomerulocystic kidney disease, ESRD, Child A B S T R A C T Corresponding Author: Shanjida Sharmim Address: Department of Pediatric Nephrology, (BSMMU), Dhaka, Bangladesh. E-mail: shanjidasharmim@gmail. com ِCitation Sharmim Sh, Huque SS, Uddin GM, Begum A, Akbar R, Hossain D. Glomerulocysic Kidney Disease and End- sage Renal Disease in a Child: A Rare Case Report and Literature Review. Journal of Pediatric Nephrology. 2023; 11(2):83-87. https://doi.org/10.22037/jpn.v12i2.41961 https://doi.org/10.22037/jpn.v12i2.41961 Use your device to scan and read the article online Article info: Received: 29 Apr 2022 Accepted: 20 Feb 2023 Publish: 01 Apr 2023 Introduction ilatation of Bowman space greater than 2 to 3 times of normal size is defined as the glomerular cyst [1, 2]. Roos claimed that glomerular cysts were first recognized and described by him in 1941 [3]. It was termed glomerulocystic kidney disease (GCKD) by Taxy and Filmer after 35 years [3, 4]. A kid- ney with more than 5% cystic glomeruli is referred to as glomerulocystic kidney (GCK) [2]. There are different forms of cystic diseases and most diseases may present in childhood. Autosomal dominant polycystic kidney disease (ADPKD), cystic renal dysplasia, and autosomal recessive polycystic kidney disease (ARPKD) present with variable renal dysfunction from neonatal to adoles- cence [1, 5]. GCKD is a different entity characterized by glomerular cysts and associated renal dysfunction [4]. The cortical distribution of cysts in GCKD differs from infantile polycystic renal disease (IPCD), where dilata- D