Letter to the editor
J Cardiovasc Med 2017, 18:731
Refractory idiopathic recurrent pericarditis:
treatment with interleukin-1 receptor
antagonist is an option!
Kubra Ozturk
a
, Murat Deveci
b
and Zelal Ekinci
c
a
Kocaeli University, Department of Pediatric Rheumatology,
b
Kocaeli University,
Department of Pediatric Cardiology and
c
Kocaeli Academy for Solidarity
Correspondence to Kubra Ozturk, Kocaeli University Hospital, Department of
Pediatric Rheumatology, 41380 Umuttepe Kocaeli, Turkey
Tel: +90 262 303 7500; fax: +90 262 3037003;
e-mail: ozturk1209@gmail.com
Received 11 January 2017 Revised 28 February 2017
Accepted 3 March 2017
To the Editor
We read with a great interest the systemic review about
the treatment of idiopathic recurrent pericarditis (IRP)
with anakinra.
1
We would like to share our experience
with anakinra in an adolescent with IRP under current
discussions of the treatment options.
A 17-year-old boy was admitted to Pediatric Cardiology
Department with complaints of chest pain and dyspnea.
His medical history was unremarkable, except for the
past 18 months, during which he had eight similar epi-
sodes of chest pain that were responsive to NSAIDs and
each one lasting for 3–7 days. He was treated with
colchicine for the last episode for 3 months. Physical
examination showed shortness of breath, an increased
heart rate (118 beats/min), and deep heart sounds.
Laboratory tests showed an increase in acute-phase reac-
tants. Echocardiography revealed moderate pericardial
effusion. Viral serology, C3, C4, ANA, genetic studies
testing for familial Mediterranean fever, and tumor
necrosis factor receptor-associated periodic syndrome
were negative. He responded well to an appropriate
dosage of ibuprofen, colchicine, and was discharged with-
out pericardial effusion. He showed a severe recurrence
after 6 weeks of wellness under colchicine and required
pericardiocentesis due to a large amount of effusion and
prednisolone which was started immediately. Two weeks
after discontinuation of prednisolone, the patient experi-
enced a new episode of pericarditis with chest pain and
increased C-reactive protein. He was treated with only
2 mg/kg/day anakinra subcutaneously with official per-
mission, because it was on off-label use. Dramatic clinical
response and normalization of the laboratory findings
within 24–48 h was achieved. Anakinra was discontinued
after a 3-month tapering period at the end of 9 months’
daily therapy. He experienced a recurrence 7 days after
anakinra discontinuation. Anakinra was restarted and an
immediate remission was held.
As previously described,
2
anakinra was used in selected
patients. Also a preliminary study
3
showed that the use of
anakinra reduced the risk of recurrence.
As a conclusion, this is a case of IRP recurring under
colchicine. Remission was held solely with anakinra with-
out steroids, NSAIDs, and colchicine during its first
usage. Early recurrence is an expected complication of
anakinra withdrawal and it should be tried with a very
long tapering dosage. Our plan is to switch alternate days
at the third month and then continue to tapper to find out
the minimal dosage to held remission.
Acknowledgements
Conflicts of interest
None declared.
References
1 Lazaros G, Imazio M, Brucato A, et al. Anakinra: an emerging option for
refractory idiopathic recurrent pericarditis: a systematic review of published
evidence. J Cardiovasc Med 2016; 17:256–262.
2 Imazio M, Brucato A, Pluymaekers N, et al. Recurrent pericarditis in children
and adolescents: a multicentre cohort study. J Cardiovasc Med 2016; 17:
707–712.
3 Brucato A, Imazio M, Gattorno M, et al. Effect of anakinra on recurrent
pericarditis among patients with colchicine resistance and corticosteroid
dependence the AIRTRIP randomized clinical trial. J Am Med Assoc 2016;
316:1906–1912.
1558-2027 ß 2017 Italian Federation of Cardiology. All rights reserved. DOI:10.2459/JCM.0000000000000520
© 2017 Italian Federation of Cardiology. All rights reserved.