Case Report Dental Prosthetic Treatments in Cleidocranial Dysplasia: Case Report and Literature Review Yosra Mabrouk , 1 Sinda Ammar, 1 Amel Labidi, 1 Lamia Mansour, 1 and Sonia Ghoul 2 1 Removable Prosthetics Department, ABCDF Laboratory (LR12ES10), Faculty of Dental Medicine, University of Monastir, Tunisia 2 ABCDF Laboratory (LR12ES10), Faculty of Dental Medicine, University of Monastir, Tunisia Correspondence should be addressed to Yosra Mabrouk; mabroukyosra@gmail.com Received 26 March 2020; Revised 30 October 2020; Accepted 9 December 2020; Published 21 December 2020 Academic Editor: Giuseppe Alessandro Scardina Copyright © 2020 Yosra Mabrouk et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. Cleidocranial dysplasia (CCD) is a rare inherited skeletal syndrome. There is no consensus regarding the dental treatment strategy. Objectives. To report a rare case of cleidocranial dysplasia and to summarize the current clinical and dental features and prosthetic treatment of similar CCD patients reported in the literature. Results. A 17-year-old girl was diagnosed with CCD. She had a short stature with the ability to bring the shoulders under the chest. All remaining teeth were deciduous except the four first molars were permanent. The maxilla was hypoplastic with a relative prognathism of the mandible. The cone-beam computed tomography examination showed a distorted and incomplete root formation of the permanent teeth. She was treated with both, complete and partial, removable overdentures. PubMed was used for the literature research using the following keys words “Cleidocranial Dysplasia”[Mesh], “Prosthodontics”[Mesh], “Dental Care”[Mesh], “cleidocranial dysostosis,” and “dental treatment.” The retention of deciduous teeth was described in the majority of cases. All the patients had supernumerary teeth. The most used treatments were dental prosthetics and orthodontics. The fixed prosthetic implant was the most used type of prosthetic treatment. Among the 15 cases who specified the type of prosthetic treatment, seven patients received removable dentures. Prosthetics was indicated especially for aged patients. Conclusion. Removable prostheses are a good solution that rapidly restores esthetics and functions. The use of implants for these patients needs to be validated by a long-term follow-up. 1. Introduction Cleidocranial dysplasia (CCD) is a rare disease that occurs in 1 per million individuals worldwide [1]. It is a disorder involving an abnormal development of bones and teeth. This dysplasia affects the entire skeleton [2] and leads to several abnormalities threatening the patient’s life. Diagnosis is always based on the clinical and radiological features and could be confirmed by a genetic analysis. The bone-related manifestations include clavicular apla- sia or hypoplasia and cone-shaped thorax with short ribs. The cephalic region presents a delayed closure of sutures and fontanels with the presence of wormian bones, frontal bossing, hypertelorism, and an enlarged nose base with a depressed bridge [3]. The tooth-related manifestations are considered as major characteristics of CCD which are almost the cause of com- plaint. The common dental features are the retention of deciduous dentition, the presence of many supernumerary teeth, and the noneruption of permanent dentition. Other disruptions could be described such as the underdevelop- ment of maxilla, upward and forward mandibular rotation, and skeletal class III malocclusion tendency. Although the presence of such problems, the child patient may have no pain, no swelling problems, and no difficulties for oral func- tions as long as deciduous teeth are still in the mouth. Child patients do not consult at an early age. Dental disability begins later with the progressive damage of deciduous denti- tion. Oral deterioration becomes rapidly progressive in few years giving the patient an edentulous and aged facial appear- ance [4]. At that time, the majority of patients consult with a complex clinical picture. Several therapeutic approaches have been reported in the literature including the surgical procedure combined or not with orthodontics or implant placement and the prosthodon- tic procedure including a removable or fixed denture. Hindawi Case Reports in Dentistry Volume 2020, Article ID 8910798, 8 pages https://doi.org/10.1155/2020/8910798