https://doi.org/10.1177/0003489419866219
Annals of Otology, Rhinology & Laryngology
1–5
© The Author(s) 2019
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DOI: 10.1177/0003489419866219
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Case Report
Introduction
West Nile virus (WNV) is a neurotropic mosquito-borne
virus of the genus Flavivirus that circulates between birds
(the amplifying hosts) and mosquitoes (mainly Culex pipi-
ens) feeding on birds. Humans and other mammals (espe-
cially horses) are considered accidental dead-end hosts.
1
WNV was first isolated in humans in Uganda in 1937.
2
The virus has spread in the last 20 years, also becoming
common in Europe, the Middle East, North America, and
East Asia, and causing disease outbreaks.
3-5
Although the
total number of WNV cases differ from year to year, in the
USA more than 2500 cases were reported to the Centers for
Disease Control and Prevention (CDC) in 2018, confirming
that WNV is the leading cause of arboviral diseases in this
continental area.
6
Furthermore, in Europe, over 2080 WNV
cases and 180 deaths were reported to the European CDC in
2018, exceeding, by far, the total number from the previous
7 years (n = 1832); compared to 2017, there was a 7.2-fold
increase.
7
In Italy, WNV is now considered endemic in sev-
eral regions, and the infectious peak usually occurs in
August and September.
8
In most cases, humans infected with WNV are asymp-
tomatic, but the infection can become clinically manifest –
usually with flu-like symptoms – in approximately 20% of
cases.
9
WNV infection can develop as a neuroinvasive dis-
ease in less than 1% of patients, especially among the
elderly or immunocompromised.
10
The fatality rate for neu-
roinvasive WNV disease has been estimated at around 20%;
patients who survive can develop severe and long-term neu-
rological sequelae.
11
Sensorineural hearing loss (SNHL) has occasionally
been reported in association with WNV infection. Here we
describe two new cases of SNHL with balance disorders
caused by WNV infection. For the first time, these patients’
vestibular function was also investigated using videonys-
tagmography (VNG). Both patients gave their written per-
mission for clinical case publication. Data were examined
in accordance with Italian privacy and sensitive data laws as
well as the in-house regulations of Padova University’s
Otolaryngology Section.
866219AOR XX X 10.1177/0003489419866219Annals of Otology, Rhinology & LaryngologyParrino et al
case-report 2019
1
Department of Neuroscience DNS, Otolaryngology Section, Padova
University, Padova, Italy
2
Unit of Tropical and Infectious Diseases, Azienda Ospedaliera- Padova
University, Padova, Italy
Corresponding Author:
Gino Marioni, MD, Department of Neuroscience DNS, Otolaryngology
Section, University of Padova, Padova, Italy.
Email: gino.marioni@unipd.it
Cochlear-Vestibular Impairment due
to West Nile Virus Infection
Daniela Parrino, MD
1
, Giuseppe Brescia, MD
1
, Maria Vittoria Trimarchi, MD
1
,
Giulia Tealdo, MD
1
, Lolita Sasset, MD
2
, Anna Maria Cattelan, MD
2
,
Roberto Bovo, MD
1
, and Gino Marioni, MD
1
Abstract
Objectives: West Nile virus (WNV) has been spreading over the last 20 years. Human infection is asymptomatic in most
cases. When the disease becomes clinically manifest, it may involve a range of issues, from a mild infection with flu-like
symptoms to a neuroinvasive disease. Albeit rarely, WNV-associated sensorineural hearing loss (SNHL) has also been
reported. Here we describe two new cases of SNHL and balance impairment caused by WNV infection.
Methods: The patients were investigated with repeated audiometric tests and, for the first time, videonystagmography
was also used.
Results: Unlike findings in the few other published cases, an improvement in audiometric thresholds and vestibular
function was documented in both of our patients.
Conclusions: In the light of our findings, a prospective study would be warranted on a large series of patients with WNV
infection in order: (i) to better define the epidemiology of the related cochlear-vestibular involvement; and (ii) to elucidate
the virus-related changes to peripheral and central auditory and vestibular functions.
Keywords
West Nile virus, bilateral sensorineural hearing loss, cochlear, disorders of equilibrium, vestibular