AJR:209, October 2017 767
tures similar to ICC in Western case series
[5, 6], whereas other studies found that CHC
showed intermediate clinical features with
HCC and ICC [7–9], which indicated that the
preoperative diagnosis of CHC was very dif-
ficult. The prognosis of patients with CHC
was still poor even after active interventions
and treatments, and previous studies have
shown that survival outcomes after resec-
tion of patients with CHC were poorer than
those of patients with HCC and were similar
to or worse than those of patients with ICC
[5–7, 9–11]. Furthermore, there is increas-
ing evidence suggesting that the outcomes of
liver transplants for patients with CHC were
worse than those for patients with pure HCC
[5, 12–14]. However, most often the diagnosis
of CHC was established only after tumor re-
section. Because of the overlap in the demo-
graphics of patients with CHC and patients
with HCC and patients with ICC, the indis-
tinguishable clinical traits of CHC, and poor
prognosis of CHC, a correct diagnosis of
CHC with imaging findings may have prog-
Combined Hepatocellular
Cholangiocarcinoma (Biphenotypic)
Tumors: Potential Role of
Contrast-Enhanced Ultrasound
in Diagnosis
Fei Li
1
Jing Han
1
Feng Han
1
Jian-wei Wang
1
Rong-zhen Luo
2
An-hua Li
1
Jian-hua Zhou
1
Li F, Han J, Han F, et al.
1
Department of Ultrasound, Sun Yat-sen University
Cancer Center, State Key Laboratory of Oncology in
South China, Collaborative Innovation Center for Cancer
Medicine, 651 Dongfeng Rd E, Guangzhou, Guangdong
510060, PRC. Address correspondence to J. Zhou
(zhoujh@sysucc.org.cn).
2
Department of Pathology, Sun Yat-sen University Cancer
Center, State Key Laboratory of Oncology in South China,
Collaborative Innovation Center for Cancer Medicine,
Guangzhou, Guangdong, PRC.
Gastrointestinal Imaging • Original Research
AJR 2017; 209:767–774
0361–803X/17/2094–767
© American Roentgen Ray Society
C
ombined hepatocellular cholan-
giocarcinomas (CHCs) have
been classified as a rare subtype
of primary liver malignancies
containing components of both hepatocellu-
lar carcinomas (HCCs) and intrahepatic cho-
langiocarcinomas (ICCs) [1]. CHCs are cate-
gorized into three distinct types: Type A
refers to separate neoplastic HCC and ICC
masses that exist independently; type B de-
scribes contiguous masses in which HCC
and ICC masses grow close to one another
and may combine but exist independently;
and type C is defined as an individual mass
that consists of both HCC and ICC compo-
nents and may display characteristics of
both. Most previous studies have shown that
only CHCs of type C present biphenotypic
features and traits [2–4].
There are a few studies in the literature
that discuss the clinical characteristics of
CHC, but the results of these studies dif-
fer. Investigators have reported that CHC
shared many demographic and clinical fea-
Keywords: combined hepatocellular cholangiocarcinoma
(CHC), contrast-enhanced ultrasound (CEUS), differential
diagnosis, hepatocellular carcinoma (HCC), intrahepatic
cholangiocarcinoma (ICC)
DOI:10.2214/AJR.16.17513
F. Li and J. Han contributed equally to this work.
Received October 13, 2016; accepted after revision
February 24, 2017.
Supported by the Fundamental Research Funds for the
Central Universities (no. 13ykzd25) and Scientific Research
Foundation for the Returned Overseas Chinese Scholars,
State Education Ministry, and Program for New Century
Excellent Talents in University.
OBJECTIVE. The objective of this study was to evaluate the diagnostic performance of
contrast-enhanced ultrasound (CEUS) in differentiating combined hepatocellular cholangio-
carcinomas (CHCs) from hepatocellular carcinomas (HCCs) and intrahepatic cholangiocar-
cinomas (ICCs).
MATERIALS AND METHODS. Thirty-three patients with pathologically confirmed
CHC and matched control subjects with pathologically confirmed HCC (n = 30) or ICC
(n = 32) who underwent preoperative CEUS from January 2005 to December 2015 were en-
rolled in this study. The CEUS images of the hepatic lesions were subjectively analyzed in
consensus by two radiologists. The diagnostic performances were evaluated by ROC analysis.
RESULTS. In the arterial phase, hyperenhancement was more common in CHCs (76%)
and HCCs (100%) than in ICCs (22%), whereas in the late phase marked washout was more
common in CHCs (76%) and ICCs (100%) than in HCCs (10%). Using marked washout in the
late phase to differentiate CHC from HCC, the area under the ROC curve (AUC) was 0.829,
and the sensitivity, specificity, and accuracy were 78%, 90%, and 83%, respectively. Using hy-
perenhancement in the arterial phase followed by marked washout in the late phase to distin-
guish CHC from ICC, the AUC value was 0.663, and the sensitivity, specificity, and accuracy
were 55%, 78%, and 66%.
CONCLUSION. Although the imaging features of CHC, HCC, and ICC on CEUS may
overlap, CEUS could be used in the differential diagnosis of CHC from HCC and ICC.
Li et al.
CEUS to Differentiate CHC From HCC and ICC
Gastrointestinal Imaging
Original Research
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