ORIGINAL ARTICLE
Validation of the consensus methodology algorithm for the
classification of systemic necrotizing vasculitis in Indian
patients
Aman SHARMA,
1
Tarun MITTAL,
2
Roopa RAJAN,
3
Manish RATHI,
2
Ritambhra NADA,
4
Ranjana W. MINZ,
5
Kusum JOSHI,
4
Vinay SAKHUJA,
2
and Surjit SINGH
1
Department of
1
Internal Medicine,
2
Nephrology,
3
Neurology,
4
Histopathology, and
5
Immunopathology, Postgraduate Institute of
Medical Education and Research, Chandigarh, India
Abstract
Aim: Many patients with systemic necrotizing vasculitis (SNV) satisfy classification criteria of different disease
entities when different classification systems are used. A new classification algorithm has been proposed recently
by using the American College of Rheumatology criteria, Chapel Hill Consensus Criteria (CHCC) and Sorensen
surrogate markers for a more uniform classification of patients suffering from these rare disorders.
Methods: We applied this algorithm to patients diagnosed as having systemic vasculitis between 2007 and
2011. We also analyzed the data using this algorithm by incorporating the recently proposed revised CHCC
nomenclature of vasculitis in place of the older criteria.
Results: Seventy-nine patients with SNV were studied. One patient diagnosed as microscopic polyangiitis (MPA)
had to be excluded from analysis as she had previously been diagnosed as having Behcet’s disease. All patients
of eosinophilic granulomatosis with polyangiitis (EGPA), granulomatosis with polyangiitis (GPA) and MPA
were reclassified to the same diagnostic subcategory after application of the algorithm. Three (16.7%) of 18
polyarteritis nodosa patients were unclassifiable after application of the consensus algorithm while two (11.1%)
were reclassified as MPA. All previously unclassifiable patients could be classified either as MPA or GPA after
application of the new algorithm. There was no difference in the results when the CHCC 2012 nomenclature
was used instead of the older CHCC in the consensus algorithm.
Conclusion: The new classification algorithm is a reliable method for classification of SNV for epidemiological
purposes in our population.
Key words: classification criteria, consensus methodology algorithm, diagnostic criteria, Indian, vasculitis.
INTRODUCTION
The last three decades have witnessed important land-
marks in the classification of systemic necrotizing vas-
culitis (SNV). These include the American College of
Rheumatology (ACR) classification criteria,
1
Chapel
Hill Classification Conference (CHCC) definitions,
CHCC 2012
2,3
and Sorensen’s incorporation of the
concept of “surrogate markers”
4
in the classification of
these disorders. There is considerable overlap in classifi-
cation when these criteria are applied to a given patient,
hampering comparison of epidemiological data
between centers. Recently, Watts et al.
5
have published
a consensus methodology algorithm for a more
Correspondence: Dr Aman Sharma, Assistant Professor, Depart-
ment of Internal Medicine, Postgraduate Institute of Medical
Education and Research, Chandigarh 160012, India.
Email: amansharma74@yahoo.com
© 2013 Asia Pacific League of Associations for Rheumatology and Wiley Publishing Asia Pty Ltd
International Journal of Rheumatic Diseases 2014; 17: 408–411