Malang Respiratory Journal Vol 04(02) page 234 A Rare Case of Chylothorax Manifestation of Gorham’s Dis- ease, Lymphangioma and Tuberculosis Agil Dananjay 1 , Ungky Agus Setyawan 1 , Ngakan Putu Parsama Putra 1 , Dini Rachma Erawati 2 , Artono isharanto 3 , Eviana Norahmawati 4 , Istan Irmansyah 5 1 Department of Pulmonology and Respiratory Medicine, Universitas Brawijaya, RSUD dr, Saiful Anwar Malang 2 Department of Radiology, Universitas Brawijaya, RSUD dr, Saiful Anwar Malang 3 Department of Thoracic and Cardiovascular Surgery, Universitas Brawijaya, RSUD dr, Saiful Anwar Malang 4 Department of Pathological Anatomy, Universitas Brawijaya, RSUD dr, Saiful Anwar Malang 5 Department of Orthopedic and Traumatology, Universitas Brawijaya, RSUD dr, Saiful Anwar Malang Abstract Background: Chylothorax is a rare condition caused by accumulation of chyle in the pleural cavity (2- 3%). More rare causes are Gorham's disease and tuberculosis Case: A 31-year-old male complained of swelling left arm and shortness of breath with recurrent pleural effusion. Pleural fluid analysis showed chylous. Bone survey showed osteolytic lesions of multiple bones as Gorham's disease. Thoracic CT showed left lung mass, atelectasis, massive fluidothorax, ipsilateral su- praclavicular lymphadenopathy, destructive left scapula. Needle aspiration of left humerus revealed lym- phangioma. Expert Mtb-Rif examination revealed Mtb detected. We assessed Gorham's disease, lymphan- gioma and lung tuberculosis with complication recurrent chylothorax and was treated anti-tuberculosis, anti-osteolytic and thorax catheter insertion. Conclusion: Difficult and rare case of chylothorax in one patient with Gorham’s disease and tuberculosis, is a poor prognosis. Keywords: Chylothorax, Gorham's Disease, Tuberculosis MRJ 2022; 4(02): 234-237 1. Introduction Chylothorax is a rare condition, it rep- resent about 2-3% of all pleural effusions. 1 Gorham’s disease (vanishing bone disease, phantom bone disease, or idiopathic massive osteolysis) is a rare bone disorder character- ized by progressive osteolysis with lymphatic and vascular proliferation. The incidence is very rare, with only a few hundred case re- * Corresponding author: Agil Dananjaya (akkun18@student.ub.ac.id) Department of Pulmonology and Respiratory Medicine Department, Saiful Anwar General Hospital, Universitas Brawijaya ports described in literature. 2 Lymphangio- mas are focal proliferations of well-differen- tiated lymphatic tissue presenting as multi- cystic or sponge-like accumulations. It can lead to chylous effusion. 3 Tuberculous chylo- thorax is a rare infectious disease that occurs when the thoracic duct is obstructed. 4 The case is interesting, it includes very rare cases,