854 VOLUME 11 NUMBER 9 SEPTEMBER 2010 NATURE IMMUNOLOGY
ARTICLES
Type 1 regulatory T cells (Tr1 cells) have emerged as an important
subset of CD4
+
T cells that help to control excessive inflammatory
responses
1
. The anti-inflammatory effects of Tr1 cells rely on their
secretion of interleukin 10 (IL-10), which dampens the function of
antigen-presenting cells and antigen-specific effector T cells to sup-
press tissue inflammation and autoimmunity. However, progress in
the molecular analysis and understanding of the biological functions
of Tr1 cells has been hampered by the lack of appropriate methods for
generating large numbers of IL-10-producing T cells in vitro.
IL-27, a heterodimeric cytokine of the IL-12 family, was initially sug-
gested to induce the expansion of proinflammatory T helper type 1
(T
H
1) cells by activating the transcription factors STAT1 and T-bet,
similarly to IL-12 (ref. 2). However, mice that lack the IL-27 receptor
(Il27ra
-/-
mice) develop exaggerated proinflammatory T cell responses
3
and autoimmunity
4
, which suggests that IL-27 might be directly
involved in the inhibition of tissue inflammation. Indeed, IL-27 has
been shown to be a growth and differentiation factor for Tr1 cells
5–7
. The
activation of naive CD4
+
cells in the presence of IL-27 or transforming
growth factor-β (TGF-β) plus IL-27 results in the differentiation of
IL-10-producing Tr1 cells that can potently suppress inflammation
and autoimmunity. In addition to its effects on the differentiation of
Tr1 cells, IL-27 directly inhibits the differentiation of IL-17-producing
helper T cells (T
H
17 cells)
4,8
and TGF-β-induced regulatory T cells
(T
reg
cells) positive for the transcription factor Foxp3 (ref. 5).
IL-27 drives the population expansion of Tr1 cells by inducing
the expression of IL-21, a member of the IL-2 family of cytokines,
which acts as an autocrine growth factor for Tr1 cells
9–11
. As with
IL-10, IL-21 expression was initially reported to be specific for T
H
2
cells
12
, but later studies showed that IL-21 is also produced by Tr1
cells
9
, T
H
17 cells
13
and follicular helper T cells
14
. All these cell types
produce IL-10, albeit in different amounts, which suggests that the
production of IL-21 and of IL-10 might be linked. Even though
IL-21 promotes the population expansion of T
H
17 cells
15
, Il21r
-/-
mice, like Il27ra
-/-
mice, show greater susceptibility to experimental
autoimmune encephalomyelitis (EAE), which indicates that IL-21
might have an important regulatory role in vivo
16
.
In an effort to delineate the molecular mechanisms by which IL-27
induces Tr1 cells, IL-27 was found to directly induce the transcrip-
tion factor c-Maf, which is crucial for Tr1 cell differentiation
9
. In the
absence of c-Maf, the generation and population expansion of Tr1
cells are compromised. Indeed, c-Maf directly transactivates the Il10
and Il21 promoters
9,17
. Although these findings highlight the impor-
tance of c-Maf and IL-21 for the biology of Tr1 cells, the addition of
recombinant IL-21 to naive CD4
+
T cells alone fails to generate Tr1
cells, which suggests that additional IL-27-driven molecular signals
contribute to Tr1 cell differentiation.
To explore the molecular mechanisms that account for the effects
of IL-27 in Tr1 cell differentiation, we have analyzed the gene expres-
sion of IL-27-induced Tr1 cells and found that the ligand-activated
transcription factor aryl hydrocarbon receptor (AhR) was induced by
IL-27 in Tr1 cells. Furthermore, during Tr1 cell differentiation, AhR
physically associated with c-Maf and transactivated the Il10 and Il21
1
Center for Neurologic Diseases, Brigham and Women’s Hospital, Harvard Medical School, Boston, Massachusetts, USA.
2
Biological Chemistry and Molecular
Pharmacology, Harvard Medical School, Boston, Massachusetts, USA.
3
Department of Environmental Health, Boston University School of Public Health, Boston,
Massachusetts, USA.
4
These authors equally contributed to this work. Correspondence should be addressed to V.K.K. (vkuchroo@rics.bwh.harvard.edu) or H.L.W.
(hweiner@rics.bwh.harvard.edu).
Received 5 April; accepted 1 July; published online 1 August 2010; doi:10.1038/ni.1912
The aryl hydrocarbon receptor interacts with c-Maf
to promote the differentiation of type 1 regulatory
T cells induced by IL-27
Lionel Apetoh
1,4
, Francisco J Quintana
1,4
, Caroline Pot
1,4
, Nicole Joller
1
, Sheng Xiao
1
, Deepak Kumar
2
,
Evan J Burns
1
, David H Sherr
3
, Howard L Weiner
1
& Vijay K Kuchroo
1
Type 1 regulatory T cells (Tr1 cells ) that produce interleukin 10 (IL-10) are instrumental in the prevention of tissue
inflammation, autoimmunity and graft-versus-host disease. The transcription factor c-Maf is essential for the induction of IL-10
by Tr1 cells, but the molecular mechanisms that lead to the development of these cells remain unclear. Here we show that
the ligand-activated transcription factor aryl hydrocarbon receptor (AhR), which was induced by IL-27, acted in synergy with
c-Maf to promote the development of Tr1 cells. After T cell activation under Tr1-skewing conditions, the AhR bound to c-Maf
and promoted transactivation of the Il10 and Il21 promoters, which resulted in the generation of Tr1 cells and the amelioration
of experimental autoimmune encephalomyelitis. Manipulating AhR signaling could therefore be beneficial in the resolution of
excessive inflammatory responses.
© 2010 Nature America, Inc. All rights reserved.