Ruptured descending aortic aneurysm as a complication of childhood
coarctation repair
A 48-year-old man was found unconscious with an unrecordable
blood pressure. He responded very well to fluid resuscitation. He had
a 2-week history of progressive left-sided pleuritic chest pain, radi-
ating into his left arm, and episodes of small-volume haemoptysis.
There were no infective symptoms. Apart from cigarette smoking, he
had no risk factors of venous thromboembolism. His past medical
history was only significant for aortic coarctation repair at the age of
6 when he underwent a resection of coarctation and anastomosis
without the use of a patch graft. He was unfortunately lost to
follow-up as an adult.
On examination, he was diaphoretic, hypotensive and tachycardic.
Heart sounds were dual and chest auscultation revealed minimal air
entry into the left lung. Computed tomography (CT) pulmonary
angiography revealed a large saccular aortic aneurysm arising just
proximal to the origin of the left subclavian artery measuring 7.4 cm
¥ 7.5 cm ¥ 7.1 cm. It was associated with a large left-sided
haemothorax. The left lower lobe was collapsed, likely a result of
compression of the left main bronchus between the thoracic aortic
aneurysm and pulmonary trunk. There was no evidence of aortic
dissection (Fig. 1).
A chest drain was inserted. He then underwent an endoluminal
repair of his ruptured aneurysm. Two GORE TAG thoracic
endoprostheses (W.L. Gore & Associates, Flagstaff, AZ, USA) were
deployed from the proximal descending thoracic aorta, clear of the
origin of left common carotid artery, extending to the mid descend-
ing thoracic aorta (Fig. 2). Balloon moulding was performed to the
distal, proximal and overlapping segments of the grafts. The left
subclavian origin was covered but was seen to fill via collateral
vessels. It was decided not to proceed to subclavian artery ligation or
carotid-subclavian bypass.
A repeat CT angiogram of the chest showed stable size of the left
haemothorax and no extravasation of contrast from the grafts
(Fig. 3). Following this, an evacuation of the left haemothorax via
video-assisted thoracic surgery was performed. The patient’s post-
operative course was unremarkable and he was discharged 12 days
after his endovascular aneurysm repair. He was referred for regular
outpatient follow-up.
Coarctation of the aorta occurs in approximately 4 in 10 000
live births and represents 5–8% of all congenital cardiac defects.
1
Fig. 1. Large saccular aneurysm arising at the origin of the left subclavian
artery, with a large left-sided haemothorax. Left basal pigtail drain in place.
Fig. 2. Angiogram demonstrating two endoluminal stent-grafts deployed
in the distal aortic arch and descending thoracic aorta, showing exclusion
of the aneurysm.
IMAGES FOR SURGEONS
ANZJSurg.com
© 2013 The Authors
ANZ Journal of Surgery © 2013 Royal Australasian College of Surgeons ANZ J Surg 83 (2013) 186–187