336
INTRODUCTION
Superior oblique myokymia (SOM) is a rare ocular
motility disorder characterized by unilateral par-
oxysmal oscillopsia and micro-tremor. Intermittent
contractions of the superior oblique muscle cause
torsional and vertical eye movements mainly in the
primary gaze position and in abduction. Although
Duane
1
had described unilateral rotary nystagmus,
Hoyt and Keane
2
were irst to use the term “supe-
rior oblique myokymia” as the electromyographic
recordings displayed motor unit potential bursts. The
pathophysiology is not clear but recent reports sup-
port the neurovascular compression hypothesis.
3,4
However, most patients with SOM have no under-
lying disease. Several medications have shown
promise in treating SOM. This is the irst case report
documenting symptomatic relief with Gabapentin in
SOM due to vascular compression.
CASE REPORT
A 27-year-old right-handed male presented with an
intermittent luttering sensation of his vision for 10
to 15 seconds per episode occurring 20 to 30 times
a day for 3 months. Slitlamp examination showed
intermittent torsional micro-tremor in the right eye.
Tonic intorsion of the right eye became obvious
on abduction. His examination was within normal
limits otherwise. Conventional brain magnetic
resonance imaging (MRI) showed no abnormality.
To evaluate the brainstem and trochlear nerve MRI
Fourier transform constructive interference in steady
state sequence (CISS) was used. The proximal cister-
nal segment of the trochlear nerve was seen to be
compressed by the right superior cerebellar artery
(SCA) while this was not seen on the contralateral
side (Figure 1).
The patient was started on oral carbamazepine
200 mg twice daily. On a subsequent visit, the dose
was increased to 400 mg three times daily over a
period of 2 weeks. The patient reported a noticeable
improvement in his symptoms, and carbamazepine
was discontinued due to elevation of transaminases
4 weeks later. After carbamazepine was discontin-
ued, his symptoms began to interfere with his daily
activities. Gabapentin was considered as it has the
advantage of renal elimination. With slow titration
so as to minimize sedation, gabapentin dose was
increased to 600 mg three times daily over a period
of 3 weeks, resulting in complete remission of SOM
attacks. Thereafter, the patient was able to return to
work. After 1 year gabapentin was tapered off. Over
a follow-up period of 3 years there has been no recur-
rence of SOM.
DISCUSSION
Superior oblique myokymia is a unique syndrome
characterized by episodic monocular torsional and
Neuro-ophthalmology, 33(6), 336–338, 2009
Copyright © 2009 Informa Healthcare USA, Inc.
ISSN: 0165-8107 print/ 1744-506X online
DOI: 10.3109/01658100903281724
CASE REPORT
Gabapentin and Superior Oblique Myokymia
Semai Bek, Tayfun Kasikci, Gencer Genc, and Zeki Odabasi
Department of Neurology, Gulhane Medical Academy, Ankara, Turkey
ABSTRACT
Superior oblique myokymia (SOM) is an uncommon disorder characterized by episodic monocu-
lar oscillopsia. Though the mechanism of SOM is not fully established, recent reports focus on the
role of vascular compression. Several medications have been reported to be of beneit but a stan-
dard protocol for SOM has not been established. This case report documents a complete symptom
relief in SOM with a documented vascular compression using gabapentin.
KEYWORDS: Gabapentin; superior oblique myokymia; trochlear nerve
Received 23 May 2009; revised 08 July 2009;
accepted 23 August 2009
Correspondence: Dr. Semai Bek, Gulhane Medical Faculty
Department of Neurology, Etlik Ankara TURKEY 06018. E-mail:
semaibek@yahoo.com.