European Journal of Ultrasound 14 (2001) 179 – 182
Case Report
The value of ultrasonography in interrupted inferior vena
cava with azygos continuation
IsmailMihmanli
a,
*, Nail Bulakbasi
b
, Fatih Kantarci
a
, Ibrahim Adaletli
a
,
Yuksel Pabuscu
b
a
Department of Radiology, Cerrahpasa Medical Faculty, IstanbulUni6ersity, 34300
I :
stanbul, Turkey
b
Department of Radiology, Gu¨lhane Military School of Medicine, Ankara,Turkey
Received 21 May 2001; received in revised form 30 July 2001; accepted 15 August 2001
Abstract
The cardiosplenic syndromes represent a complex set of abnormalities of the thorax and viscera resulting from
abnormal folding of the embryo during early development. Anomalies of venous development include interruption of
inferior vena cava (IVC), and in combination with situs inversus referred to as the polysplenia syndrome. We present
a 23-year-old male previously diagnosed as having a persistent left IVC on venography whereas ultrasonographic
examination clearly demonstrated interrupted IVC with azygos continuation along with situs inversus.© 2001
Elsevier Science Ireland Ltd. All rights reserved.
Keywords : Agenesis; Inferior vena cava; Ultrasonography; Situs inversus
www.elsevier.com/locate/ejultrasou
1.Case report
A 23-year-old malepresented with recurrent
thrombophlebitisof the right lower extremity.
Pelvic venography in addition to bilateral lower
extremity venographic examination showed that
the common iliac veinswere draining to a left
paravertebrally located venous structure (Fig. 1),
thought to be a persistent left inferior vena cava
(IVC). One year after the venographic examina-
tion the patient presented with abdominal discom-
fort and abdominal ultrasonography (US) showed
absence of the hepatic and infrahepatic segments
of the IVC. The hepatic veins were draining di-
rectly into the rightatrium (Fig.2). In the left
paravertebral location,a large vascular structure
draining both common iliac veins could be fol-
lowed up to the diaphragm and was diagnosed as
the azygos vein. Both renalveins were draining
into this large vascularstructure.Echocardio-
graphic examination demonstrated agenesis of the
IVC and a dilated azygos vein, which was drain-
ing into the superior vena cava, and prolapse of
the mitral and tricuspid valves. In addition to
* Corresponding author. Tel.: + 90-212-586-1586; fax: +
90-212-632-0044.
E-mail address : mihmanli@yahoo.com (I. Mihmanli).
0929-8266/01/$ - see front matter © 2001 Elsevier Science Ireland Ltd. All rights reserved.
PII: S 0 9 2 9 - 8 2 6 6 ( 0 1 ) 0 0 1 6 0 - 4