In: Chronic Myeloid Leukemia ISBN: 978-1-62948-971-1
Editors: Celalettin Ustun and Uday R. Popat © 2014 Nova Science Publishers, Inc.
Chapter XVIII
Can We Cure CML without
Transplantation?
Prithviraj Bose
*
, M.D.
1,2
and Pankit Vachhani, M.D.
2
1
Massey Cancer Center and the
2
Department of Internal Medicine, Virginia
Commonwealth University, Richmond, VA, US
Abstract
A model disease in many respects, chronic myelogenous leukemia (CML) has been
called the pristine paradigm for molecularly targeted therapy. Bcr-Abl tyrosine kinase
inhibitors (TKIs) have dramatically altered the therapeutic landscape of CML, so much
so that many patients diagnosed in chronic phase and treated appropriately now enjoy a
life expectancy similar to that of the general population. However, despite the enormous
strides made in advancing therapy for this disease, it remains, for the most part, incurable
except by allogeneic hematopoietic stem cell transplantation (HSCT). For patients, this
means a lifelong commitment to daily TKI therapy. These agents are expensive, and not
without side effects, making cure a highly desirable and worthwhile goal. Multiple
studies have shown that in contrast to their impressive efficacy against proliferating CML
cells, TKIs are unable to eradicate the tiny fraction of quiescent stem cells that are
responsible for disease persistence and recurrence upon TKI discontinuation. This has
fueled efforts to better understand CML stem cell biology and elucidate survival
pathways unique to these cells, the targeted interruption of which could potentially
synergize with Bcr-Abl TKIs to confer synthetic lethality while sparing normal
hematopoietic stem cells (HSCs). The molecular pathogenesis of CML and mechanisms
of resistance to TKIs are reviewed in detail elsewhere in this volume. In this chapter, we
provide a brief overview of these topics, summarize key concepts relating to CML stem
cell biology, and discuss strategies to effectively target this difficult-to-kill population
that might one day result in a cure for CML.
*
Address for correspondence: Prithviraj Bose, M.D., McGlothlin Medical Education Center, 1201 E Marshall St,
11
th
floor, Room 213, P.O. Box 980070, Richmond, VA 23298, USA. Email: pbose@mcvh-vcu.edu.
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