Outcomes for Soft-Tissue Sarcoma in 8249 Cases from a Large State
Cancer Registry
Juan C. Gutierrez, M.D., Eduardo A. Perez, M.D., Dido Franceschi, M.D., Frederick L. Moffat, Jr., M.D.,
Alan S. Livingstone, M.D., and Leonidas G. Koniaris, M.D.
1
DeWitt Daughtry Family Department of Surgery, University of Miami Miller School of Medicine, Miami, Florida
Submitted for publication January 30, 2007
Background and objectives. To date, outcome re-
ports for soft-tissue sarcoma (STS) have largely been
limited to single or paired institutional series. To more
accurately elucidate population-based outcomes and
prognostic factors associated with STS, a large cancer
registry was examined.
Methods. STS arising in the Florida Cancer Data
System were examined (1981–2004).
Results. A total of 8249 patients were identified, the
calculated annual incidence of sarcoma being approx-
imately 38 cases per million in 2003. The tumor histol-
ogies among these patients were leiomyosarcoma and
gastrointestinal stromal tumor (LMS/GIST) (43.5%),
malignant fibrous histiocytoma (MFH) (31.5%), liposar-
coma (19.0%), and fibrosarcoma (6.0%). Tumors were
situated in the extremities (30.7%), truncal or visceral
locations (50.4%), retroperitoneum (11.7%), and head
or neck (7.2%). Thirty-three percent of lesions were
over 10 cm in greatest dimension, while 50.2% were
classified as high grade. Median overall survival was
25 months. Superior survival was observed for liposar-
comas and fibrosarcomas as compared to MFH and
LMS/GIST (P < 0.001). Retroperitoneal and truncal
sarcomas had a more ominous prognosis than did
other sites (P < 0.001). Multivariate analysis of pre-
treatment variables demonstrated that increasing age,
male gender, non-Caucasian race, advanced stage, and
a truncal or retroperitoneal location were each inde-
pendently associated with lower survival. Histological
subtype was also an independent predictor of out-
come. Surgical resection and radiation therapy were
the only treatment variables shown to improve
survival.
Conclusions. Histological subtype, tumor site, and
stage are independent prognostic factors in STS. Sur-
gical resection and radiotherapy are unique among
treatment modalities in association with a significant
survival benefit. © 2007 Elsevier Inc. All rights reserved.
Key Words: soft-tissue sarcoma; histological sub-
types; surgery; radiotherapy; chemotherapy; prognos-
tic factors.
INTRODUCTION
Soft-tissue sarcomas (STS) are uncommon, biologi-
cally and histologically heterogeneous neoplasms aris-
ing from mesenchymal tissues throughout the body [1].
Approximately 9420 cases were diagnosed in the
United States in 2005, accounting for less than 1% of
all new malignancies [2– 4]. Traditionally, the main-
stay of treatment for STS has been surgical resection
with tumor-free margins, adjuvant or neoadjuvant che-
motherapy, and/or radiation coming into their own
with the advent of limb-, tissue-, and function-sparing
surgery [5–7]. Tumor size, grade, stage, and surgical
margin status are identified in single-institution series
as the most important prognostic factors in these tu-
mors [8 –11]. To date, treatment strategy has been
determined more by anatomical site than by histolog-
ical subtype [12]. Only recently have investigators fo-
cused significantly on the influence of histology on
prognosis [13, 14].
The sarcoma literature is dominated by retrospective
series from single institutions or pooled data from two
or more institutions with major tertiary referral prac-
tices. Such series are limited by small sample size and
selection bias in favor of advanced, recurrent, or oth-
erwise complicated sarcomas. These factors may skew
survival and other treatment outcomes in this uncom-
mon, heterogeneous group of tumors. We therefore an-
1
To whom correspondence and reprint requests should be ad-
dressed at University of Miami School of Medicine, 3550 Sylvester
Comprehensive Cancer Center, 1475 NW 12th Avenue, Miami, FL
33136. E-mail: lkoniaris@med.miami.edu.
Journal of Surgical Research 141, 105–114 (2007)
doi:10.1016/j.jss.2007.02.026
105
0022-4804/07 $32.00
© 2007 Elsevier Inc. All rights reserved.