Everolimus in Pulmonary Transplantation: Pharmacokinetics and Exposure–Response Relationships John M. Kovarik, PhD, a Gregory I Snell, MD, b Vincent Valentine, MD c Robert Aris, MD, d Charles KN Chan, MD, e Heinz Schmidli, PhD, a and Ulrich Pirron, PhD a Background: In this study we evaluated exposure, safety and efficacy data from an international trial of everolimus. We sought to identify a tolerated and efficacious range for blood levels of this agent in maintenance lung transplant recipients. Methods: In a randomized, double-blind, multicenter trial, 213 maintenance lung transplant recipients received either everolimus 1.5 mg twice daily (n = 101) or azathioprine 1 to 3 mg/kg/day (n = 112) with cyclosporine and corticosteroids. At 15 visits over the first 2 years of the trial, we obtained 826 everolimus trough (C 0 ) blood samples. We used median-effect analysis to assess relationships between everolimus C 0 vs efficacy and safety responses. Results: Everolimus administration began at 1.5 mg twice daily and was progressively lowered over the first 2 months to an average of 1.2 0.4 mg twice daily, which was maintained thereafter. This dose yielded median C 0 levels of 6.6 ng/ml (10th to 90th percentiles: 2.8 to 11.8 ng/ml). Over this range of everolimus C 0 , freedom from a decline in pulmonary function with bronchiolitis obliterans syndrome and freedom from biopsy-proven acute rejection were both 88%. The incidence of increased cholesterol (6.5 mmol/liter), increased triglycerides (2.9 mmol/liter) and transiently decreased platelet count (100 10 9 /liter) rose significantly with increasing C 0 . Infections and drug-related adverse events were not significantly related to exposure. Conclusions: A tolerated and efficacious concentration range for everolimus in maintenance lung transplantation appears to be 3 to 12 ng/ml when used in conjunction with cyclosporine and corticosteroids. This range should be prospectively assessed with possible refinement as more clinical experience is gained. J Heart Lung Transplant 2006;25:440 – 6. Copyright © 2006 by the International Society for Heart and Lung Transplantation. Chronic allograft dysfunction and rejection are major challenges in the care of lung transplant recipients. In lung transplantation, chronic dysfunction manifests as obliterative bronchiolitis due to fibroproliferation and leads to an inexorable decline in pulmonary function. Given the difficulties in the histologic diagnosis of obliterative bronchiolitis, bronchiolitis obliterans syn- drome (BOS) can be considered the best available surrogate marker for obliterative bronchiolitis and is predictive of graft and patient survival. 1 BOS is charac- terized clinically by progressive airflow obstruction on the basis of pulmonary function tests. There is currently no treatment that can prevent the development or progression of obliterative bronchiolitis or BOS. Everolimus is an immunosuppressant for the preven- tion of acute allograft rejection after kidney and heart transplantation. 2 Everolimus inhibits growth factor– stimulated proliferation of lymphocytes and mesenchy- mal cells 3,4 and proliferation of human lung fibroblasts in vitro. 5 Given the fibroproliferative processes under- lying obliterative bronchiolitis, a role for everolimus in preventing the decline of pulmonary function and onset of BOS in maintenance lung transplant recipients was assessed in a 3-year multicenter, randomized, double- blind clinical trial comparing everolimus with azathio- prine. 6 In brief, the protocol-specified primary study end-point was an efficacy failure composite of 15% decline in forced expiratory volume in 1 second (FEV 1 15%), graft loss, death or loss to follow-up 12 months after the first dose. The incidence of efficacy failure was significantly lower in the everolimus group compared with the azathioprine group (21.8% vs 33.9%, p = 0.046). Other end-points significantly reduced with everolimus included change from baseline FEV 1 15%, change from baseline FEV 1 15% with BOS, and acute From a Novartis Pharmaceuticals, Basel, Switzerland; b Alfred Hospital, Melbourne, Australia; c Ochsner Clinic Foundation, New Orleans, LA, USA; d University of North Carolina at Chapel Hill, Chapel Hill, NC, USA; e University of Toronto, Toronto, Ontario, Canada Submitted July 21, 2005; revised November 29, 2005; accepted December 10, 2005. Reprint requests: John M. Kovarik, PhD, Clinical Pharmacology, Novartis Pharmaceuticals, Building WSJ 103.426, Basel 4002, Swit- zerland. Tel: 41-061-324-8239. Fax: 41-061-324-3074. E-mail: john. kovarik@novartis.com Copyright © 2006 by the International Society for Heart and Lung Transplantation. 1053-2498/06/$–see front matter. doi:10.1016/ j.healun.2005.12.001 440