Summary
The presence of immunoglobulin crystal inclusions in
plasma cells from plasmacytomas and B-NHLs (linked
to overstimulation and overproduction) has been fre-
quently reported. Our case describes a lymphoplasma-
cellular synovitis in a patient with osteoarthritis (OA)
showing an unusually high plasma cell infiltration and
for the first time crystals in plasma cells. Using im-
munohistochemistry, these crystals were identified as
being IgG with a balanced lambda/kappa ratio.
IgV
H
gene analysis (n = 5 clones) showed that they
were somatically mutated (R/S of CDR > 3); in one
case, an insertion of 9 nucleotides on the CDR2 region
was observed. High R/S values in the CDR indicated
antigen selectivity and affinity (4/5).
Since no germinal centers could be detected and the
analyzed B cells showed antigen selectivity, it may be
concluded that already antigenically activated B cells
migrated into the synovium and locally differentiated
into plasma cells, leading to the extensive infiltration
observed.
Rheumatoid fibroblasts were shown to support termi-
nal B cell differentiation. Our data suggests that the abil-
ity of fibroblasts to activate B cells is not only restricted
Teaching Case
Extensive Plasma Cell Infiltration
with Crystal IgG Inclusions and Mutated IgV
H
Gene
in an Osteoarthritis Patient with
Lymphoplasmacellular Synovitis. A Case Report*
Raquel Magalhães
1
, Thorsten Gehrke
2
, Maria M. Souto-Carneiro
3
,
Jörg Kriegsmann
4
, Veit Krenn
1
1
Institute of Pathology, Charité, Humboldt University Berlin,
2
ENDO-Klinik, Hamburg,
3
National Institute of Arthritis Musculoskeletal and Skin Diseases, NIH Bethesda;
4
Gemeinschaftspraxis für Pathologie, Trier
Pathol. Res. Pract. 198: 45–50 (2002) 0344-0338/02/198/1-45 $15.00/0
PATHOLOGY
RESEARCH AND PRACTICE
© Urban & Fischer Verlag
http://www.urbanfischer.de/journals/prp
to RA, but also occurs in OA. The intense plasma cell
infiltration contributed to further cartilage damage by
altering the microenvironment of the nourishing syn-
ovial tissue or by the local production of pathogenic au-
toantibodies.
Key words: Plasma cells – Osteoarthritis – Crystal in-
clusions – IgV
H
genes
Abbreviations: B-NHL = B lymphocyte non Hodgkin lym-
phoma; IgVH = immunoglobulin variable heavy chain; R/S,
replacement to silent mutation ratio; CDR = complementarity
determining region; FR = framework region; RA = rheumatoid
arthritis
Introduction
Accumulation of plasma cells and B-lymphocytes is a
constant phenomenon of long standing synovitis in au-
toimmune (rheumatoid arthritis, reactive arthritis, psori-
atic arthritis) and degenerative joint diseases [11, 18,
27].
Address for correspondence: Veit Krenn, Institute for
Pathology of Charité, Humboldt University Berlin, Schu-
mannstr. 20–21, 10115 Berlin, Germany.
Tel.: +49 (0)30/45053-6134, Fax: +49 (0)30/45053-6907.
E-mail: veit.krenn@charite.de
* The present work was supported by the SFB 421(Protektive
und pathologische Folgen der Antigenverarbeitung)