TRENDS in Neurosciences Vol.24 No.9 September 2001
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508 Opinion Opinion
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Opinion Opinion
Developmental dyslexia is traditionally defined
1
as ‘a
disorder in children who, despite conventional
classroom experience, fail to attain the language
skills of reading, writing and spelling commensurate
with their intellectual abilities’. Dyslexia researchers
have focused on two alternative hypotheses: the
phonological deficit account
2–4
, which holds that the
reading difficulties derive initially from problems in
breaking spoken words down into their constituent
sounds (syllables or phonemes), and the
magnocellular deficit account, which holds that the
reading problems derive from impaired sensory
processing, caused by abnormal auditory
5
and/or
visual
6,7
magnocellular pathways.
Unfortunately, in spite of extensive research, these
approaches have failed to account for the full range of
difficulties established for dyslexic children. It is
therefore timely to present the case for our
alternative hypothesis that the full range of deficits
might be accounted for in terms of cerebellar deficit.
There is no space here to survey the rich evidence
relating to alternative hypotheses. We fully expect the
commentators to present cogent alternative data and
views. In preview, we claim that:
(1) The behavioural symptoms of dyslexia can be
characterized as difficulties in skill automatisation
8,9
(the process by which, after long practice, skills
become so fluent that they no longer need conscious
control).
(2) The pattern of difficulties in cognitive,
information processing and motor skills is predicted
by the cerebellar deficit hypothesis
9–12
.
(3) Dyslexic adults showing the above behavioural
manifestations of cerebellar impairment also show
direct neurobiological evidence of cerebellar
impairment
13
. This is consistent with other evidence
of cerebellar abnormalities in dyslexia
14
.
A TINS debate – Hindbrain versus the
forebrain:a case for cerebellar deficit
in developmental dyslexia
Progressive improvement in reading and writing skills, through school and beyond, is something that many of us take for granted.
However, for people suffering from dyslexia, these skills are not acquired in the usual manner. For many years it has been thought that
brain differences in the cortical areas related to language are the likely source of the problems. However, it has recently been
established that the problems associated with this syndrome go beyond reading-related problems: balance, motor skills and sensory
processes can also be affected. An explanation for this multitude of seemingly disparate problems has proved elusive. Roderick
Nicolson, Angela Fawcett and Paul Dean believe that a deficit in cerebellar performance might provide a complete explanation, and it is
this argument, presented in the first article below, that forms the focus of this debate. But can cerebellar deficit explain all deficits
experienced by dyslexics? Are those that experience cerebellar damage later in life similarly affected? Is the cerebellum the sole
contributor to dyslexia?
Two pairs of experts in this field, Thomas Zeffiro and Guinevere Eden, and Richard B. Ivry and Timothy C. Justus, discuss these and
other questions. It becomes clear during the debate that the acquisition of reading-related skills requires the co-ordination of many
areas of the brain involved in visual, motor and cognitive activities, and that an increased understanding of dyslexia could provide
insights far beyond the disorder itself. The conclusion to this debate is provided by Roderick Nicolson and his colleagues.
Developmental
dyslexia:the cerebellar
deficit hypothesis
Roderick I. Nicolson, Angela J. Fawcett
and Paul Dean
Surprisingly, the problems faced by many dyslexic children are by no means
confined to reading and spelling. There appears to be a general impairment in
the ability to perform skills automatically, an ability thought to be dependent
upon the cerebellum. Specific behavioural and neuroimaging tests reviewed
here indicate that dyslexia is indeed associated with cerebellar impairment in
about 80% of cases. We propose that disorders of cerebellar development can
in fact cause the impairments in reading and writing characteristic of
dyslexia, a view consistent w ith the recently appreciated role of the
cerebellum in language-related skills. This proposal has implications for early
remedial treatment.