RESEARCH ARTICLE Supramaximal Verification of Peak Oxygen Uptake in Adolescents With Cystic Fibrosis Maarten S. Werkman, PT, MSc; Hendrik J. Hulzebos, PT, PhD; Pauline B. van de Weert-van Leeuwen, MSc, MD; Hubertus G.M. Arets, PhD, MD; Paul J.M. Helders, PT, PhD; Tim Takken, PhD Child Development & Exercise Center, Wilhelmina Children’s Hospital, University Medical Center Utrecht, Utrecht, the Netherlands (Mr Werkman and Drs Hulzebos, Helders, and Takken); and Cystic Fibrosis Center and Department of Pediatric Respiratory Medicine, Wilhelmina Children’s Hospital, University Medical Center Utrecht, the Netherlands (Drs van de Weert-van Leeuwen and Arets). Purpose: To study whether peak oxygen uptake (V . O 2 peak ), attained in traditional cardiopulmonary exercise testing (CPET) in adolescents with cystic fibrosis (CF), could be verified by a supramaximal exercise test. Methods: Sixteen adolescents with CF (forced expiratory volume in 1 second as % of predicted [range, 45%-117%]) volunteered and successively performed CPET and a supramaximal test (Steep Ramp Test [SRT] protocol). Results: Cardiopulmonary exercise testing and the SRT resulted in comparable cardiorespiratory peak values. We found no significant difference in oxygen uptake (V . O 2 peak /kg) between CPET and the SRT (38.9 ± 7.4 and 38.8 ± 8.5 mL min 1 kg 1 , respectively; P = .81). We found no systemic bias for CPET and SRT measurements of V . O 2 peak /kg and no differences between CPET and SRT V . O 2 peak values within and between the maximal and non-maximal effort groups (P > .4). Conclusion: The V . O 2 peak measured in CPET seems to reflect the true V . O 2 peak in adolescents with CF. (Pediatr Phys Ther 2011;23:15–21) Key words: adolescents, cystic fibrosis, exercise testing, exercise tolerance, pulmonary ventilation INTRODUCTION AND PURPOSE Exercise testing is increasingly used to evaluate the level of exercise capacity and to define training inten- sity in adolescents with chronic lung diseases like cys- tic fibrosis (CF). 1,2 Cardiopulmonary exercise testing (CPET) is currently accepted as the gold standard to study a patient’s aerobic capacity and possible limiting factors. 2,3 Most clinical exercise testing is performed with 0898-5669/110/2301-0015 Pediatric Physical Therapy Copyright c 2011 Wolters Kluwer Health | Lippincott Williams & Wilkins and Section on Pediatrics of the American Physical Therapy Association. Correspondence: H.J. Hulzebos, PT, PhD, Child Development & Ex- ercise Center, Wilhelmina Children’s Hospital, Room KB.02.056, Uni- versity Medical Center Utrecht, PO Box 85090, 3508 AB Utrecht, The Netherlands (H.Hulzebos@umcutrecht.nl). Grant Support: This study was funded by an unconditional research grant (DO-IT) from the Scientific College Physiotherapy of the Royal Dutch Society for Physiotherapy (Wetenschappelijk College Fysiother- apie, Koninklijk Nederlands Genootschap voor Fysiotherapie) and an unrestricted grant from the Dutch Cystic Fibrosis Society. DOI: 10.1097/PEP.0b013e318208ca9e progressive workloads during cycle ergometer or tread- mill exercise. During both tests, cardioventilatory parame- ters such as peak oxygen uptake (V . O 2 peak ), peak workload (W peak ), peak heart rate (HR peak ), and the ratio of carbon dioxide production to oxygen consumption (respiratory exchange ratio [RER]) can be calculated using gas analysis of expired air. 4 The most important parameter of exercise capacity is the V . O 2 peak . 2,3,5 Maximum oxygen uptake (V . O 2 max ) is considered to be the maximum attainable oxygen uptake by the cardiorespiratory and neuromuscular system, re- sulting in a ˙ VO 2 plateau at the end of testing despite a further increase in workload. 6,7 Furthermore, V . O 2 peak is defined as the highest level of oxygen uptake attained dur- ing a single test without necessity of a plateau of the ˙ VO 2 curve. 8 Questions can be raised about the validity of that attained ˙ VO 2peak during CPET in adolescents with CF, be- cause reduced exercise capacity during CPET in adoles- cents with CF compared with peers without the disease has been reported. 9-12 However, the observed peak heart rates in these studies were lower than values observed in ado- lescents without CF. Therefore, this lower V . O 2 peak might be due to an actual lower V . O 2 peak or to an incapability of CPET to reach real V . O 2 peak in adolescents with CF. This Copyright © 2011 Wolters Kluwer Health | Lippincott Williams & Wilkins and Section on Pediatrics of the American Physical Therapy Association. Unauthorized reproduction of this article is prohibited. Pediatric Physical Therapy Verification of ˙ Vo 2peak in CF 15