C OMMENT
TIG NOVEMBER 1998 VOL. 14 NO. 11
438 0168-9525/98/$ – see front matter © 1998 Elsevier Science All rights reserved.
PII: S0168-9525(98)01579-0
Genetics is a science of the aberrant.
By studying mutant alleles, we hope
to understand better the wild-type
function of a gene. The more alleles
analyzed for a specific gene, the
greater the functional spectrum that
is acquired. The only limitation is
generating the alleles to form a series.
Historically, this has been easy in
phage, bacteria, yeast and fruit flies,
simply because it is practical and
economical to produce vast numbers
of these organisms, yet mouse geneti-
cists have been hesitant to attempt
such experiments owing to financial
and temporal constraints. Nowadays,
however, there are many ways to
generate allelic series relatively
quickly and cheaply in the mouse.
The advent of gene targeting
1
cleared the path for rapid, directed
mutagenesis and has yielded a
treasure-trove of new mouse alleles,
most of which are knock-outs. But
the null mutation coupled with the
wild-type hardly constitutes an allelic
series. To increase the diversity, it is
possible to recapitulate subtle alleles
by homologous recombination in the
mouse
2,3
. Gene targeting can also be
used to incorporate the recombinase-
recognition sequences loxP and frt
interspersed among exons, so that a
single transgenic mouse can spin off
a variety of allelic progeny when
mated with appropriate recombi-
nase-expressing mouse lines. Such
‘allelogenic’ mice have recently been
used to create novel alleles of Fgf8, a
fibroblast growth factor gene
4
, and
N-myc, a proto-oncogene
5
. This strat-
egy can produce hypomorphic alleles
that allow for phenotypic analysis
at later developmental stages that
would have been precluded by the
early-death phenotype of the null
mutation.
However, if a more classical
approach is preferred – or one would
rather study point mutations than
recombinase-induced deletions –
there is always chemical mutagenesis.
The point mutagen ethylnitrosourea
6
can induce missense mutations in the
mouse, often allowing a gene prod-
uct to retain some residual function.
A benefit of this strategy is that the
investigator does not need any mol-
ecular knowledge of the gene to build
a series (i.e. there is no need to worry
about what type of an engineered
point mutation will generate a hypo-
morph versus a hypermorph versus a
neomorph versus an amorph). In
fact, the gene itself doesn’t even have
to be cloned. Instead, chemical
mutagenesis allows for a random
mutational spectra to unfold, unen-
cumbered by any preconceived and
limited notions of the observer. In a
simple screen, the germ cells of a male
are mutagenized and then the mouse
is mated with a series of females that
are already homozygous mutant for
the gene of interest (usually a null
mutation). Newly induced alleles from
the male will fail to complement the
female’s genotype and the progeny
will be recognizable as mutants. This
scheme, called the specific locus test,
can rapidly generate an extensive
allelic series
7
. In fact, since the 1950s,
specially designed test stocks of mice
have been used in large-scale specific
locus tests at the Oak Ridge National
Laboratory to determine the muta-
genicity of different types of radiation
and chemicals
8
. The result of these
massive screens have been literally
hundreds of alleles at seven specific
loci, two of which are dilute and
short-ear.
In a second type of screen, de-
letion stocks, currently those that
occur at coat-color loci, have been
used for rapidly generating point
mutations by chemical mutagenesis
to form an allelic series in the func-
tional units, restricted to the deleted
segment
9,10
. Nowadays, chromosome
engineering in the mouse can create
deletions at any defined site in the
genome
11,12
. Additionally, these de-
letions can be purposefully marked
with coat-color genes that allow the
manipulated chromosomes to be fol-
lowed throughout the crosses
13
. By
applying chemical mutagenesis to
Mouse alleles: if you’ve seen one, you haven’t seen them all
ALLAN PETER DAVIS AND MONICA J. JUSTICE
davisap@bio.ornl.gov • mjustice@bcm.tmc.edu
LIFE SCIENCES DIVISION, OAK RIDGE NATIONAL LABORATORY, OAK RIDGE, TN 37831-8080, USA.
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