Correspondence 333
© 2006 The Authors
Journal Compilation © 2006 International Society of Neuropathology • Brain Pathology
A 4-YEAR-OLD GIRL WITH MASS IN THE
FRONTOTEMPORAL BONE
Contributed by: Shanop Shuangshoti
1
;
Sukruthai Mujananon
1
;
Krishnapundha Bunyaratavej
2
;
Mookda Chaipipat
1
; Surachai Khaoroptham
2
1
Department of Pathology and
2
Division of
Neurosurgery, Department of Surgery, Faculty of
Medicine, Chulalongkorn University, Bangkok,
Thailand.
CLINICAL HISTORY
A 4-month-old female infant presented
with a growing extracranial mass at the
left frontotemporal region. Covered
with intact skin, the lesion measured
3.5 × 3 × 3 cm; it was well-defined, bony
hard in consistency, and fixed to the under-
lying skull. There were no other abnormal
symptoms, and routine laboratory tests
were within normal limits. The mass
appeared sclerotic on skull film. Comput-
erized tomography scan of the brain
(Figure 1A) showed a homogeneously
enhancing expansile bone tumor. The
lesion caused widening of the lower part of
the left coronal suture, just above the
orbital roof. The patient underwent left
frontotemporal craniotomy, and the mass
was found to involve the frontal and tem-
poral bones, around the inferior limb of
the coronal suture, adherent to the under-
lying dura. The orbital roof and apex
were also affected. The lesion was totally
resected. The immediate postoperative
course was uneventful.
On gross inspection of the fresh speci-
men, the mass was hard and showed gray
tan cut surfaces (Figure 1B).
MICROSCOPIC FINDINGS
Intraoperative smears and imprints
disclosed bimodal population of large
melanin-containing epithelial cells and
smaller neuroblast-like cells (Figure 2). The
former possessed abundant pale eosino-
philic cytoplasm, whereas the latter
appeared as round naked nuclei with finely
dispersed chromatin pattern. Thick clus-
ters of fibrovascular tissue were also evi-
dent. An intraoperative diagnosis was
rendered. Permanent sections subsequently
confirmed the diagnosis by demonstrating
lobules of monotonous small round cells
(Figure 3A), and pigmented epithelial cells
with glandular formation (Figure 3B).
Mitotic figures were rarely observed, 0–1/
10 high-power field (HPF). Immunohis-
tochemically, the small round tumor cells
expressed synaptophysin (Figure 4A),
while the pigmented epithelial cells were
reactive for cytokeratin (Figure 4B) and
HMB-45 (Figure 4C).
CORRESPONDENCE: Reader Submitted Case Reports
Edited by Dr Ronald L. Hamilton
Figure 1.
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Figure 2.
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Figure 4.
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