Akdoğan A, Eroğlu A, Kutanis D, Cekic B (2016) Anesthetic Management in a Patient with Congenital Insensitivity to Pain Syndrome for Lower Extremity Surgery. Int J Anesth Res. 4(10), 340-342. 340 OPEN ACCESS http://scidoc.org/IJAR.php International Journal of Anesthesiology & Research (IJAR) ISSN 2332-2780 Anesthetic Management in a Patient with Congenital Insensitivity to Pain Syndrome for Lower Extremity Surgery Case Report Akdoğan A, Eroğlu A * , Kutanis D, Cekic B Karadeniz Technical University, Anesthesiology and Intensive Care Medicine, Trabzon, Turkey. *Corresponding Author: Ahmet Eroglu, Karadeniz Technical University, Anesthesiology and Intensive Care Medicine, Trabzon, Turkey. E-mail: aheroglu@hotmail.com Received: July 04, 2016 Accepted: October 13, 2016 Published: October 18, 2016 Citation: Akdoğan A, Eroğlu A, Kutanis D, Cekic B (2016) Anesthetic Management in a Patient with Congenital Insensitivity to Pain Syndrome for Lower Extremity Surgery. Int J Anesth Res. 4(10), 340-342. doi: http://dx.doi.org/10.19070/2332-2780-1600070 Copyright: Eroğlu A © 2016. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution and reproduction in any medium, provided the original author and source are credited. Introduction Congenital insensitivity to pain (CIP), irst described by Dearborn in the year 1932, is a rarely encountered neuropathic syndrome that manifests itself starting from birth and is characterized by unresponsiveness to painful stimulants, anhydrous, mental retardation, and recurring feverish episodes [1]. The cases usually involve painless fractures, inger, lip and tongue injuries, neurogenic arthropathies (Charcot joint), and joint deformities that could lead to chronic osteomyelitis [2]. The mortality rate of the disease is very high due to the fact that there is no speciic treatment that could be administered. The subjects are usually deceased by the time they reach their adolescence. In cases where the subjects are required to go through a surgical procedure, in spite of the fact that the patient is unresponsive to pain, it would still be necessary to administer anesthesia to prevent unwanted circumstances such as tactile hyperesthesia. We would like to present our experiment regarding anesthesia management under Bispectral index (BIS) monitoring in a patient with congenital insensitivity to pain for lower extremity procedure due to osteomyelitis. Case Presentation The plastic surgery clinic planned to operate on a 16 year old 60 kg male patient in ASA II group suffering from congenital insensitivity to pain and diagnosed previously with osteomyelitis development in the left patellar region (Figure 1). In the preoperative assessment of the patient, the laboratory values and lungs were normal. The patient, who was subjected to physical examination, was insensitive to pain and temperature and displayed slight mental retardation. His other neurologic examination results and his sense of touch were normal. The airway evaluation revealed Mallampati classiication to be III and sternomental distance to be 10 cm, while the neck movements were determined to be restricted. Prior to the procedure, the patient’s family members were informed of the anesthesia method to be applied and the potential risks and their consent was obtained. Fiberoptic bronchoscope, laryngeal mask and tubes of various Abstract Congenital insensitivity to pain (CIP) is a rarely syndrome and is characterized by unresponsiveness to painful stimulants, anhydrous, mental retardation, and recurring feverish episodes. In this case report we presented our anesthesia management in a patient with congenital insensitivity to pain for lower extremity surgery due to osteomyelitis. Keywords: Congenital Insensitivity to Pain (CIP) Syndrome; Anesthesia; Lower Extremity Surgery.