METHODS IN PATHOLOGY
Examination of Tumor and Tumor-Like Conditions of Bone
Hanh Khuu, MD, Daniel Moore, MD, Scott Young, PA, Kenneth A. Jaffe, MD,
and GeneP. Siegal, MD, PhD
Surgical pathology specimens composed of bone, ranging from core biopsy to limb
amputation specimens, require special attention, processing, and often unique
equipment. This readily translates into additional handling steps and time, espe-
cially when one factors in clinical correlation with the surgeon and radiologic
review of all images with a knowledgeable musculoskeletal radiologist. When these
factors are superimposed on the rarity of these lesions in routine practice, it is not
surprising that most trainees, as well as seasoned pathologists, are wary of these
lesions. In this report, we use a case of osteofibrous dysplasia (Campanacci's
disease) to demonstrate the dissection of such a surgical specimen and complete
the report with a brief discussion of the entity.
Ann Diagn Pathol 3: 364-369, 1999. Copyright © 1999 by W.B. Saunders Company
Index Words: Bone neoplasm, bone tumor, osteofibrous dysplasia, gross examina-
tion
B
ONES involved by neoplastic processes when submit-
ted as surgical pathology specimens require special
treatment and handling. Because these specimens are
obtained by different techniques (from needle core
biopsies to forequarter amputations), they result in
vastly different specimens for malignant skeletal tu-
mors. Many pathologists, irrespective of their training
and experience, are wary of these specimens because of
their rarity in practice. In addition, bone lesions may be
especially challenging secondary to overlapping histo-
logic appearance. Additional equipment is required (ie,
a band saw) and decalcification is invariably needed.
Few descriptions of dissection techniques for bone speci-
mens have been reported. 1-3In this presentation, we use
the example of a case from our practice to demonstrate
the standard techniques we use to dissect a bony
specimen, ultimately reaching a final diagnosis. No
attempt is made to be encyclopedic and it is clearly
recognized that the bone or bones involved, the size of
the lesion, the involvement of surrounding soft tissues,
From the Division of Anatomic Pathology, Department of Pathology, the
Musculoskeletal Radiology Section,DepartmentofRadiology, and the Division of
OrthopaedicSurgery,Departmentof Surgery, Universityof Alabama at Birming-
ham,
Supported in part by a grantfrom the Pediatric Oncology Group through
National Cancer Institute, National lnstitutes ofHealth (CA 25408).
Address reprint requeststo GeneP. Siegal, M_D,PhD, Division of Anatomic
Pathology,DepartmentofPathology,506 KrackeBldg, UniversityofAlabama at
Birmingham, Birmi@am, AL 35233.
Copyright© 1999 by W..B. Saunders Company
1092-9134/99/0306-0005510.00/0
and the vital organs all affect the approach to examining
the specimen grossly, sectioning it appropriately, and
submitting it for final processing.
Case Report
A 15-year-old girl presented with a lesion of the left tibia
that had been previously biopsied at an outside institution and
initially diagnosed as being "consistent with fibrous dysplasia."
The patient was referred to our institution for surgical
consultation. The biopsy material was reviewed, but no radio-
graphic films or reports were available. A diagnosis of benign
fibro-osseous lesion consistent with fibrous dysplasia was
rendered and the differential diagnosis was discussed with the
orthopedist. After the radiographic images were reviewed (see
below), the patient underwent partial resection of the left
tibia, including the area of concern.
Radiographic Description
Review of the radiographic images with the musculoskeletal
radiologists demonstrated a multiloculated radiolucent expan-
sion of the anterolateral cortex of the tibia. An associated
anterior bowing with minimal cortical thickening and sclerosis
was noted. The radiographic features of the lesion were felt to
be most typical of osteofibrous dysplasia. Although possible,
fibrous dysplasia was thought to be a much less likely entity in
this case given the cortically based location of the lesion.
Gross Description
A certified pathologist's assistant with significant experi-
ence in dealing with musculoskeletal tumors "grossed in" the
specimen after discussion with the attending orthopedic pa-
thologist and joint review of the radiographs to determine in
364 Annals of Diagnostic Pathology, Vol 3, No 6 (December), 1999: pp 364-369