Introduction
Adult patients with acute lymphoblastic leukemia (ALL) have
a poorer outcome than children, characterized by a higher relapse
and shorter survival rate. This difference in survival has been par-
ticularly highlighted for older adolescents and young adults (AYAs)
with ALL with an age range of 16 to 20 years who may end up
being treated with either pediatric or adult regimens.
1
A recent
study of more than 300 AYAs showed significantly better event-
free and overall survival when AYAs received therapy according to
pediatric protocols rather than adult programs.
2
There are several
factors to explain these results, including social, disease-specific,
and treatment-related features. In the aforementioned analysis,
a comparison between the regimens showed that the children’s
protocols incorporated earlier and more intensive central nervous
system (CNS) prophylaxis and higher cumulative doses of the
nonmyelosuppressive components such as vincristine, steroids,
and asparaginase. Numerous studies have since been reported
using such “pediatric-like” protocols in younger adults whereby the
upper age limit for these approaches has been extended to 40 years
and higher.
3-7
The hyper-CVAD (cyclophosphamide/vincristine/doxorubicin/
dexamethasone) program is a well-established regimen for the treat-
ment of adult patients with ALL.
8
Up to 8 cycles of fractionated
cyclophosphamide, vincristine, doxorubicin, and dexamethasone
alternating with high-dose methotrexate and cytarabine are followed
by a prolonged standard maintenance with interspersed cycles of
Abstract
Augmented Hyper-CVAD Based on Dose-
Intensified Vincristine, Dexamethasone, and
Asparaginase in Adult Acute Lymphoblastic
Leukemia Salvage Therapy
Stefan Faderl, Deborah Ann Thomas, Susan O’Brien, Farhad Ravandi, Guillermo
Garcia-Manero, Gautam Borthakur, Alessandra Ferrajoli, Srdan Verstovsek,
Mohamed Ayoubi, Michael Rytting, Jennie Feliu, Hagop M. Kantarjian
The prognosis of adult patients with relapsed acute lymphoblastic leukemia (ALL) remains poor. Recent studies in adoles-
cents and young adults reported better outcomes when therapy was intensified. Based on hyper-CVAD (cyclophospha-
mide/vincristine/doxorubicin/dexamethasone) as a backbone, we designed an augmented version with intensified doses of
vincristine, dexamethasone, and asparaginase (L-asparaginase in the first 62 patients and pegaspargase in the remainder)
starting from course 1. Ninety patients have been enrolled, with a median age of 34 years (range, 14-70 years). Most
patients (78%) had pre-B ALL and were in first salvage (76%), with a first remission duration of 12.6 months (range, 1-78
months). Ten patients had primary refractory disease. Of 88 evaluable patients, 41 (47%) achieved complete remission (CR),
with a median time to CR of 29 days (range, 18-80 days). Eight patients (9%) died within the first 30 days. Median CR dura-
tion, progression-free survival, and overall survival were 5, 6.2, and 6 months, respectively. Median overall survival of CR
patients was 10.2 months (range, 1.4-69.5+ months). Twenty-eight patients (32%) proceeded to stem cell transplantation.
Myelosuppression-associated complications were frequent. Pegaspargase was equally effective and easier to administer
than L-asparaginase. Augmented hyper-CVAD may be suitable to be studied in younger adults with untreated ALL.
Clinical Lymphoma, Myeloma & Leukemia, Vol. 11, No. 1, 54-59, 2011; DOI: 10.3816/CLML.2011.n.007
Keywords: ALL, Chemotherapy, Myelosuppression, Pegaspargase
Original Study
Department of Leukemia, The University of Texas M.D. Anderson Cancer Center,
Houston, Texas
Submitted: Aug 3, 2010; Revised: Sep 18, 2010; Accepted: Sep 24, 2010
Address for correspondence: Stefan Faderl, MD, Department of Leukemia, Unit
428, The University of Texas M.D. Anderson Cancer Center, 1400 Holcombe Blvd,
Houston, TX 77230-1402
Fax: 713-792-9616; e-mail: sfaderl@mdanderson.org
2152-2650/$ - see frontmatter
© 2011 Elsevier Inc. All rights reserved.
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Clinical Lymphoma, Myeloma & Leukemia February 2011
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