Nanomedicine (Lond.) (Epub ahead of print) ISSN 1743-5889 part of Research Article 10.2217/nnm-2016-0430 © 2017 Future Medicine Ltd Aim: Our goal was to improve vincristine (VCR) based rhabdomyosarcoma (RMS) therapy by encapsulating the drug into liposomes. A targeting strategy was attempted to enhance tumor accumulation. Materials & methods: VCR was loaded in control and peptide-decorated liposomes via an active method. The interaction of an RMS-specific peptide with the presumed target furin and the cellular uptake of both liposomal groups were studied in vitro. Pharmacokinetics and biodistribution of VCR-containing liposomes were assessed in an RMS xenograft mouse model. Results: Liposomes ensured high VCR concentration in plasma and in the tumor. Peptide- decorated liposomes showed modest uptake in RMS cells. Conclusion: The investigated peptide-modified liposomal formulation may not be optimal for furin-mediated RMS targeting. Nevertheless, VCR-loaded liposomes could serve as a delivery platform for experimental RMS. First draft submitted: 23 December 2016; Accepted for publication: 14 March 2017; Published online: 27 April 2017 Keywords:฀ biodistribution฀•฀furin฀•฀liposomes฀•฀peptide฀•฀pharmacokinetic฀ •฀rhabdomyosarcoma฀•฀targeting฀•฀vincristine Rhabdomyosarcoma (RMS) is the most com- mon pediatric soft tissue sarcoma, account- ing for approximately 10% of all solid can- cers in children [1] and is subdivided into two main histological groups, embryonal RMS and alveolar RMS (aRMS) [2] . Embryonal RMS arises in around 60–70% of all patients and has a rather good prognosis. In contrast, aRMS represents the more aggressive subtype and is associated with the poorer prognosis, with a 5-year survival below 30% [3,4] . The first-line therapy for RMS is based on a combination of chemotherapeutics, includ- ing vincristine (VCR), followed by radiation therapy or surgery [4] . However, suboptimal pharmacokinetic properties of VCR, such as short half-life and large volume of distribu- tion, preclude an optimal application of this agent [5] . It has been shown that encapsulation of VCR in liposomes prolongs its circulation time and improves its therapeutic efficacy in leukemia tumor models [6,7] . In fact, Mar- qibo ® , a sphingomyelin/cholesterol-based liposomal VCR formulation, was clinically approved by the US FDA in 2012 for the treatment of acute lymphoblastic leukemia in second or greater relapses [5] . The phar- macokinetic parameters and biodistribution of liposomal VCR have been determined in mice-bearing solid tumors, such as human epidermoid carcinoma A431 [8] and MX-1 human mammary adenocarcinoma [9] . Fol- lowing liposomal VCR injection, its circu- lation time was prolonged resulting in sig- nificantly higher VCR concentration in the tumors for all time points tested. This can be attributed to the enhanced permeability and retention (EPR) effect [10] , a result of unique pathophysiological features of some solid tumors such as defective vascular architecture and extensive angiogenesis [11] . Lower clear- Prolonged circulation and increased tumor accumulation of liposomal vincristine in a mouse model of rhabdomyosarcoma Maurizio Roveri 1,2,3 , Alice Pfohl 1,2,3 , Patricia Jaaks 1,2 , Nagjie Alijaj 1,2 , Jean- Christophe Leroux 3 , Paola Luciani* ,‡,3,4 & Michele Bernasconi** ,‡,1,2 1 Experimental฀Infectious฀Diseases฀&฀ Cancer฀Research,฀University฀Children’s฀ Hospital฀Zurich,฀8008฀Zurich,฀Switzerland 2 Children’s฀Research฀Center,฀University฀ Children’s฀Hospital฀Zurich,฀8032฀Zurich,฀ Switzerland 3 Department฀of฀Chemistry฀&฀Applied฀ Biosciences,฀Institute฀of฀Pharmaceutical฀ Sciences,฀ETH฀Zurich,฀8093฀Zurich,฀ Switzerland 4 Department฀of฀Pharmaceutical฀ Technology,฀Institute฀of฀Pharmacy,฀ Friedrich฀Schiller฀University,฀07743฀Jena,฀ Germany *Author฀for฀correspondence:฀ paola.luciani@uni-jena.de **Author฀for฀correspondence:฀ michele.bernasconi@kispi.uzh.ch Authors฀contributed฀equally For reprint orders, please contact: reprints@futuremedicine.com