over, we could not find another example of the uniformly ex- pansile intradiploic cystic appearance of the temporal bony lesion seen in our patient. A similar appearance has been reported by Abdelwahab et al., 13 but their patient had an occipital bony lesion. CT has been recognised to be the mainstay of diagnosis of this entity, 9 particularly when it reveals the “ground glass” appearance in typical locations. Whereas this observation appears generally valid, there may be a role of MR imaging in certain uncommon situations. For example, in cystic fibrous dysplasia, the radiolu- cent appearance especially in long bones may mimic malignant lesions such as intraosseous sarcomas. 17 MR imaging clearly distinguishes these 2 entities. 12 In our patient, both the CT and MR studies unequivocally suggested a benign, long-standing disease process. Numerous entities need to be considered in the differ- ential diagnosis of such intradiploic cystic lesions, including an- eurysmal bone cyst, unicameral cyst, nonossifying fibroma, osteochondroma, giant cell and eosinophilic granulomas, intradi- ploic epidermoids, osteoblastomas as well as sarcomatous neo- plasms. 8;9;11;14;15 Cystic degeneration is an uncommon but well-described phe- nomenon in fibrous dysplasia. Cystic degeneration may place these lesions somewhere along the spectrum between simple and aneurismal bone cysts, as suggested by Ferretti et al. 18 The clinical importance of this phenomenon in fibrous dysplasia is the rela- tively rapid increase in size that may be observed, and was also evident in our patient. This may lead to the lesion being misdi- agnosed on clinical grounds as an aneurysmal bone cyst, simple cyst or even sarcomatous change in a pre-existing benign bony tumour. Cystic degeneration in fibrous dysplasia needs to be better recognised as a cause for this. The management clearly rests on the recognition of this entity as a benign one. This may not always be straightforward, with atypical clinical and radiological presentations such as cystic change. Al- though it has been reported that there is no firm evidence for clinical arrest or resolution with onset of bony maturation, 4 most do recommend postponing surgical intervention till late adoles- cence. 4;5;15 Even then, it should be limited to cosmetic debulking. 19 In case of diagnostic doubt, or when considering a potentially malignant lesion it makes sense to achieve a histological diagnosis. This should be especially borne in mind if one is contemplating any radical surgery for a suspected malignant swelling. Even when one is suspecting monostotic fibrous dysplasia, it is recommended to have a biopsy. 4;5;15 In the polyostotic form, the multiple lesions make a presumptive diagnosis of fibrous dysplasia much more accurate. Additional measures necessary for all patients having fibrous dysplasia of the temporal bone include periodic otological examinations, owing to the high probability of compromise of the external canal, and other secondary complications. 5 It should be noted that there is no role for radiation therapy, owing to the high incidence (upto 44%) of malignant transformation. 20 To conclude, cystic fibrous dysplasia should be considered in the case of any temporal intradiploic expansile lesion. Cystic degeneration may result in the rapid growth, and this may be misleading and result in suspicion of malignant transformation. 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Oral Surg Oral Med Oral Pathol Oral Radiol Endod 1999; 88: 337–342. 19. Waldron CA. Fibro-osseous lesions of the jaws. J Oral Maxillofac Surg 1993; 51: 828–835. 20. Slow IN, Friedman EW. Osteogenic sarcoma arising in a pre-existing fibrous dysplasia: report of a case. J Oral Surg 1971; 29: 126–129. Dyke–Davidoff–Masson syndrome manifested by seizure in late childhood: a case report Kenjiro Ono 1 MD PHD MD PHD, Kiyonobu Komai 2 MD PHD MD PHD, Takayuki Ikeda 3 MD PHD MD PHD 1 Department of Neurology, Tsuruga City Hospital, Tsuruga, Fukui, Japan, 2 Department of Neurology and Neurobiology of Aging, Kanazawa University Graduate School of Medical Science, Kanazawa, Japan, 3 Department of Internal Medicine, Tsuruga City Hospital, Tsuruga, Fukui, Japan Summary The patient was a 19-year-old woman who presented with hemiatrophy and diminished superficial sensation on the left side of her body including her face. 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