© Kamla-Raj 2015 Int J Hum Genet, 15(2): 61-72 (2015)
Knowledge, Awareness and Participation of Medical and
Non-medical Students in the Malaysia National
Thalassemia Prevention Programme
Vasudeva Murthy C.R.
1
, Muhammad Zarif Asraf Bin Zulkeflle
2
,
Sunil Pazhayanur Venkateswaran
3
and Ankur Barua
4
1,3
Department of Pathology,
4
Department of Community Medicine,
International Medical University, Kuala Lumpur, Malaysia
2
Biomedical Science Graduate, Management and Science University, Shah Alam, Malaysia
KEYWORDS Screening. Attitudes. Thalassemia. Multi-racial Population
ABSTRACT There are about 1 in 20 Malaysians who are carriers of the thalassemia gene and the prevalence of
this disease in Malaysia is 6-10 percent. This study was conducted to assess knowledge, awareness and participation
of medical and non-medical students in the Malaysia National Thalassemia Prevention Programme. The design of
the study was a cross-sectional study. A total of 300 questionnaires were distributed to selected students from the
university. The collected data was analysed using SPSS version 20.0. Data analysis revealed a highly significant
difference in total knowledge between medical students and non-medical students and the thalassemia awareness
also showed significant statistical association between medical and non-medical students. In conclusion, medical
students have better knowledge, awareness and screening rate of thalassemia.
Address for correspondence:
Dr. Vasudeva Murthy C.R.
Department of Pathology,
International Medical University,
Kuala Lumpur, Malaysia
Telephone: 03-2727 7430
Fax: +603-8656 7229 / 8656 8018
E-mail: drvasu2001@gmail.com
INTRODUCTION
Thalassemia is one of the most common ge-
netic blood disorders in the world. There are
approximately 240 million people worldwide who
are heterozygous for β-thalassemia and approx-
imately 200,000 affected homozygotes are born
annually (Haque et al. 2015). It is a genetic disor-
der which involves the absence of or errors in
genes that affect the body’s ability to produce a
protein in the red blood cells called haemoglo-
bin, a protein present in the red blood cells. Gen-
erally, these groups of single gene disorders have
an estimated 5 percent prevalence as carriers.
Like in many other countries, thalassemia also
poses an important public health problem in
Malaysia. Approximately 4.5 of Malaysians are
carriers of ß-thalassemia, and annually the af-
fected births are estimated at 2.1 per 1,000 with
an estimated 5,600 patients with transfusion de-
pendent ß-thalassemia in Malaysia (George and
Tan 2010). The Malaysian Chinese possess the
Southeast Asian deletion that causes Bart’s hy-
dropsfetalis, a fatal condition in α-thalassemia
(Fucharoen and Vip 2009). Lifelong treatment is
needed for those affected with symptomatic
thalassemia major and intermedia. Population
screening for detection of carriers is the best
way to reduce its occurrence and is being prac-
ticed in many countries. The best mechanism
for screening varies as it covers various areas
such as the genetic examination and analysis as
well as genetic counselling.
In several countries, carrier screening pro-
grams are being conducted using various ap-
proaches. They include cascade screening,
screening of ‘high-risk’ communities, screening
of the general population and antenatal screen-
ing. The percentage of β-thalassemia carriers
identified using a cascade screening approach
is 5-6 times higher. It has been shown earlier that
in communities where consanguinity is common,
one can identify even more number of carriers.
More than 90 percent of the “at risk” couples
were identified in Sardinia using cascade screen-
ing by examining only 11percent of the popula-
tion (Sazlina et al. 2015).Thalassemia carrier
screening programmes can be divided into large-
ly mandatory programmes and voluntary pro-