136 https://oamjms.eu/index.php/mjms/index
Scientifc Foundation SPIROSKI, Skopje, Republic of Macedonia
Open Access Macedonian Journal of Medical Sciences. 2021 Aug 24; 9(C):136-139.
https://doi.org/10.3889/oamjms.2021.7002
eISSN: 1857-9655
Category: C - Case Reports
Section: Case Report in Surgery
Perioperative Approach in a Patient with Myasthenia Gravis
Saimir Kuci
1
* , Alfred Ibrahimi
1
, Shaban Memeti
2
, Marsela Goga
1
, Selman Dumani
3
, Ali Refatllari
3
1
Department of Cardiac Anesthesia, Mother Teresa University Hospital Center, Tirana, Albania;
2
University Clinic of Paediatric
Surgery, Faculty of Medicine, Ss Cyril and Methodius University of Skopje, Skopje, Republic of Macedonia;
3
Department of
Cardiac Surgery, Mother Teresa University Hospital Center, Tirana, Albania
Abstract
BACKGROUND: Myasthenia gravis is an autoimmune neuromuscular disorder that causes the destruction and
overall decrease in functional acetylcholine receptors at the neuromuscular junction. The resultant respiratory and
cardiovascular implications are a primary cause of mortality; therefore, a complete and comprehensive understanding
of this disorder is vital for the anesthesia provider. Anesthesia management in myasthenia gravis is a great challenge
for all anesthesiologists. In this disease, even small doses of muscle relaxants could lead to delayed recovery for
respiratory muscles.
CASE REPORT: We present the case of a 38 years old woman (weight 87 kg) diagnosed with Myasthenia Gravis,
which symptoms have worsened recently. The case demonstrates the anesthetic challenges involved, with a focus
on the overall approach, pharmacologic considerations, physiological changes, and an emphasis on preoperative
operative and post-operative optimization.
CONCLUSION: Thymectomy is a common procedure performed in cases of myasthenia gravis (MG) with a thymoma
or general MG that does not improve with medical therapy. During anesthesia, the use of propofol or sevofurane with
opioids without the use of any neuromuscular blocking agents has been used with success.
Edited by: Igor Spiroski
Citation: Kuci S, Ibrahimi A, Memeti S, Goga M,
Dumani S, Refatllari A. Perioperative Approach in a
Patient with Myasthenia Gravis. Open Access Maced J
Med Sci. 2021 Aug 24; 9(C):136-139. https://doi.org/10.3889/
oamjms.2021.7002
Keywords: Thymecomy; Myasthenia gravis;
Neuromuscular disorder
*Correspondence: Saimir Kuci, Department of Cardiac
Anesthesia, Mother Teresa University Hospital Center, Rr.
Dibres 372, Tirane, Albania. E-mail: saimirkuci@gmail.com
Received: 05-Aug-2021
Revised: 12-Aug-2021
Accepted: 14-Aug-2021
Copyright: © 2021 Saimir Kuci, Alfred Ibrahimi,
Shaban Memeti, Marsela Goga, Selman Dumani,
Ali Refatllari
Funding: This research did not receive any fnancial
support
Competing Interests: The authors have declared that no
competing interests exist.
Open Access: This is an open-access article distributed
under the terms of the Creative Commons Attribution-
NonCommercial 4.0 International License (CC BY-NC 4.0)
Introduction
The incidence of myasthenia gravis (MG) is
cited as 50–142 cases per 1 million or 0.25 to 2.0
per 100,000 population [1], [2]. Gender discrepancy
is present, and women 20–30 years of age are
most often afected, followed by men who are often
older than 60 years of age when their disease
presents [1]. The disease is a chronic autoimmune
disorder characterized by a decrease in acetylcholine
receptors at the neuromuscular junction secondary
to their destruction or inactivation by circulating
antibodies [1]. Muscular weakness, fatigability, and
rapid exhaustion especially after repetitive voluntary
muscle use, as with exercise, are the hallmark signs
of the disorder. Four Stages of the disease have
been classifed based on the severity of muscular
involvement and range from self-limiting extraocular
muscle involvement Stage I to severe whole-body
generalized muscular weakness Stage IV [3]. Patients
are at an increased risk of pulmonary aspiration
because of pharyngeal and laryngeal muscle
weakness, and they may present with dysphagia,
dysarthria, and an overall difculty of handling
secretions. Cardiovascular involvement usually
occurs and manifests in atrial fbrillation, heart block,
and cardiomyopathy, with the presented case having
hypertension as the only known cardiovascular
manifestation.
Myasthenia gravis has historically been a
challenging disease for the anesthetist to manage
because of its involvement in the pulmonary, muscular, and
cardiovascular systems as well as with drug interactions.
Case Report
An 87-kg, 168-cm, 38-year-old woman
presented with the main complaint of weakness of the
entire limbs nausea, and vomiting then blurred vision for
7–8 months, symptoms that have worsened recently.
On physical examination, there was right ptosis. Muscle
strength based on the MRC scale was 3. After Neurologist
consultation and tests that were made including
rapid nerve stimulation examination, which showed a
decremental decrease of >10% in the abductor muscles
of the minimi digit, trapezius, and right ocular orbicularis
the patient was diagnosed with Myasthenia Gravis.
Chest CT scan was performed showing a
visible heterogeneous mass with contrast enhancement