Copyright © 2015 Wolters Kluwer Health, Inc. All rights reserved.
C
URRENT
O
PINION
Bone and morphogenetic protein signalling and
muscle mass
Roberta Sartori
a,b
and Marco Sandri
a,b,c
Purpose of review
The purpose of this study is to discuss the involvement of bone and morphogenetic proteins (BMPs) in the
control of muscle mass.
Recent findings
The transforming growth factor-beta (TGFb) superfamily comprises a large number of secreted proteins that
regulate a variety of fundamental biological processes. Sequence similarities define two ligand subfamilies:
the TGFb/Activin subfamily and the BMP subfamily. Within the members of TGFb subfamily, myostatin
emerged as the most critical ligand that affects muscle size and function. Indeed, mutations that inactivate
Myostatin lead to important muscle growth in animals and humans. However, recent findings have
increased the complexity of the TGFb superfamily. Indeed, two independent groups have shown that BMP
pathway, acting through Smad1/5/8, is the fundamental hypertrophic signal and dominates Myostatin
signalling. Moreover, BMP-Smad1/5/8 negatively regulates a novel ubiquitin ligase, named MUSA1 that
is required for muscle loss. This article reviews the rapid progress made in the last year regarding the
signalling downstream TGFb superfamily and its involvement in the homeostasis of adult muscle fibres.
Summary
The recent insights gained into the interplay of TGFb and BMP signalling in muscle have challenged our
pre-existing ideas of how the adult skeletal muscle phenotype is regulated in health and disease.
Keywords
activin, bone and morphogenetic protein, MUSA1, muscle atrophy, muscle hypertrophy, myostatin, Smad
INTRODUCTION
Skeletal muscle mass and muscle fibre size may vary
according to physiological and pathological con-
ditions. An increase in muscle mass and fibre size,
that is muscle growth or hypertrophy, occurs during
development, in response to mechanical overload
and/or anabolic hormonal stimulation. Cellular and
protein turnover contribute to hypertrophy with
different degree. During development and in early
postnatal life, the growth of skeletal muscle, such as
the mass of any other tissue, depends primarily on
cellular turnover and secondarily on protein syn-
thesis [1]. Conversely, in adulthood, the regulation
of muscle mass and fibre size essentially reflects
protein turnover, namely the balance between
protein synthesis and degradation within the
muscle fibres [2]. One of the most important
anabolic signal is the insulin-like growth factor 1
(IGF1)-phosphoinositide-3-kinase (PI3K)-AKT/pro-
tein kinase B (PKB) pathway that controls both
protein synthesis and protein degradation. IGF1-
Akt promotes not only muscle growth but
also prevents muscle atrophy during catabolic
conditions. Many signals coming from integrins
and extracellular matrix, sex hormones, beta adre-
nergic stimulation, nutrients, energy levels and
inflammation with inflammatory cytokines con-
verge on this pathway. One of the upstream signals
that has been reported to impinge on IGF/AKT
signal and that exerts a great effect on muscle mass
regulation is the transforming growth factor-beta
(TGFb) signalling. Myostatin is the most famous
member of TGFb superfamily and myostatin inhi-
bition leads to a massive muscle growth that, how-
ever only partially depends on IGF1/AKT axis.
Recent data on bone and morphogenetic proteins
a
Dulbecco Telethon Institute, Venetian Institute of Molecular Medicine,
b
Department of Biomedical Sciences, University of Padova, Padova and
c
Telethon Institute of Genetics and Medicine (TIGEM), Napoli, Italy
Correspondence to Marco Sandri, Department of Biomedical Sciences,
University of Padova, Dulbecco Telethon Institute, Venetian Institute of
Molecular Medicine (VIMM), Viale Orus 2 35129 Padova, Italy. Tel: +39
049 7923258; fax: +39 049 7923250; e-mail: marco.sandri@unipd.it
Curr Opin Clin Nutr Metab Care 2015, 18:215–220
DOI:10.1097/MCO.0000000000000172
1363-1950 Copyright ß 2015 Wolters Kluwer Health, Inc. All rights reserved. www.co-clinicalnutrition.com
REVIEW