Original article
Total esophagogastric dissociation in adult neurologically impaired patients
with severe gastroesophageal reflux: an alternative approach
E. J. Hazebroek,
1
F. W. J. Hazebroek,
2
S. Leibman,
1
G. S. Smith
1
1
Department of Upper Gastrointestinal Surgery, Royal North Shore Hospital, Sydney, NSW, Australia; and
2
Department of Pediatric Surgery, Erasmus MC-Sophia Children’s Hospital, Rotterdam, the Netherlands
SUMMARY. Patients with neuromuscular impairment, such as cerebral palsy or myotonic dystrophy, often suffer
from oropharyngeal neuromuscular incoordination and severe gastresophageal reflux (GER). In 1997, Bianchi
proposed total esophagogastric dissociation (TEGD) as an alternative to fundoplication and gastrostomy to
eliminate totally the risk of recurrence of GER in neurologically impaired children. Little information exists about
the best management for adult patients with severe neurological impairment in whom recurrent GER develops after
failed fundoplication. We present our experience in three adult patients with neurological impairment in whom
TEGD with Roux-en-Y esophagojejunostomy and feeding gastrostomy was performed for permanent treatment of
GER.
KEY WORDS: esophagogastric dissociation, gastresophageal reflux, neurologically impaired.
INTRODUCTION
Patients with neuromuscular impairment, such as
cerebral palsy or myotonic dystrophy, often suffer
from oropharyngeal neuromuscular incoordination
and severe gastroesophageal reflux (GER). The
prevalence of GER in children with severe neurologi-
cal impairment is reported to be between 33% and
75%.
1,2
Fundoplication and gastrostomy may be
effective in facilitating nutrition, reducing the risk of
aspiration pneumonia, and thus improving quality
of life of these patients. However, the incidence of
failure of the fundoplication in neurologically
impaired children with subsequent recurrence of
symptoms has been reported to be between 5% and
25%.
3,4
Recurrence rates after redo-fundoplication
are even higher than the initial operation and carry a
greater risk of complications.
5,6
In 1997, Bianchi pro-
posed total esophagogastric dissociation (TEGD) as
an alternative to fundoplication and gastrostomy to
eliminate totally the risk of recurrence of GER in
neurologically impaired children.
7
More recently, it
has been suggested that TEGD can be used as a
primary treatment of choice for severely neurologi-
cally impaired children who are experiencing GER
and are completely dependent on tube feeds.
8,9
Little information exists about the best manage-
ment for adult patients with severe neurological
impairment in whom recurrent GER develops after
failed fundoplication.
This report considers the potential role of TEGD
with Roux-en-Y esophagojejunostomy and feeding
gastrostomy for permanent treatment of GER in
adult patients with neurological impairment.
CASE REPORTS
Between 2004 and 2007, TEGD with Roux-en-Y
esophagojejunostomy and feeding gastrostomy was
performed in three adult patients with neurologically
impairment. The procedure is performed through an
upper midline abdominal incision. After mobilization
of the left liver lobe, access to the gastroesophageal
junction (GEJ) is obtained. If previous fundoplica-
tion was performed, the wrap is unravelled. The
proximal part of the stomach is mobilized by division
of the left gastroepiploic vessels and short gastric
vessels. After isolation of the subdiaphragmatic
esophagus, the esophagus is transected above the
Address correspondence to: Dr Garett Smith, MS FRACS,
Department of Upper Gastrointestinal Surgery, Level 2, Vindin
House, Royal North Shore Hospital, St. Leonards, Sydney,
NSW 2065, Australia. Email: garetts@med.usyd.edu.au
Diseases of the Esophagus (2008) 21, 742–745
DOI: 10.1111/j.1442-2050.2008.00834.x
© 2008 Copyright the Authors
Journal compilation © 2008, Wiley Periodicals, Inc. and the International Society for Diseases of the Esophagus 742