TIBS 17 - AUGUST 1992
clones. The encoded suppressor pro-
teins appear to act at a wide range of
sites in the cell's growth-regulating cir-
cuitry. In the particular case of RB and
its cousin p107, a locus of action seems
to be right in the midst of the switches
- the cyclin-CDKs - which run the cell
cycle clock. The weight of current evi-
dence suggests that the cyclin-CDK
components of this clock represent
the evolutionary ancient heart of the
machinery. With the advent of metazoa,
this clock needed to be entrained with
additional extracellular growth-regu-
lating signals. The two proteins, RB and
p107, would seem to have been invented
to couple the exogenous signals with
the progression of the clock, imposing a
new layer of control on this already
well-developed machinery. Loss of RB
function may decouple the clock from
its usual physiological regulators, allow-
ing a reversion to a more primitive state
in which the clock advances unhin-
dered. We are within a year or two of
understanding most of this, reducing
speculative model building to solid
unimpeachable facts.
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The 'ins' and 'outs' of mitochondrial
membrane channels
MITOCHONDRIA are the site of the key
reactions of energy metabolism in eukary-
otes, by which free energy associated
with the oxidation of foodstuffs is used
to drive ATP synthesis. These reac-
tions, which occur at the innermost of
the two mitochondrial membranes, are
generally believed to involve ion gradi-
ents across this membrane. Thus, the
integrity of the mitochondrial inner
membrane as a permeability barrier to
ions is a basic tenet of Mitchell's chemi-
osmotic hypothesis 1. There is consider-
able evidence that the transport of
metabolites and inorganic ions across
the inner membrane is highly regulated,
involving either electrically neutral sys-
tems (such as the di- and tricarboxylic
acid carriers) which do not affect the
membrane's electrical gradients, or
electrogenic systems (such as those for
ADP/ATP exchange and Ca2+ influx)
which are driven by the same electrical
gradients.
The outer mitochondrial membrane,
which is not directly involved in the
reactions of oxidative phosphorylation,
C. A. Mannella is at the Wadsworth Center for
Laboratories and Research, New York State
Department of Health, Empire State Plaza,
Box 509, Albany, NY 12201-0509, USA and
the School of Public Health, University of
Albany, State University of New York, USA.
© 1992, Elsevier Science Publishers, (UK)
The outer membrane of the mitochondrion contains thousands of copies
of a pore-forming protein called VDAC or porin. Considerable progress has
been made towards elucidating the molecular structure of this channel.
Moreover, mounting evidence that the permeability of VDAC may be regu-
lated is challenging the textbook notion of the outer membrane as a simple
sieve. Numerous other channel activities have been detected by electro-
physiological approaches in both the outer and inner mitochondrial mem-
branes. The inner-membrane channels do not appear to be open under
normal physiological conditions and so should not dissipate energy-trans-
ducing ion gradients. The biological functions of the different classes of
mitochondrial channels are uncertain, but several possibilities (including
protein translocation) are being explored.
is the lone permeability barrier between
the energy-transducing inner mem-
brane and the cytosol. Conventional
wisdom is that the outer membrane is a
simple sieve, allowing free passage of
ions and metabolites smaller than 1 or 2
kDa, but not of larger macromolecules.
This article highlights recent findings
about channels in the outer and inner
membranes of mitochondria, discover-
ies that are causing a re-examination of
set notions about the permeability of
these membranes. (For a recently pub-
lished compilation of mini-reviews, see
Ref. 2.)
VDAC, the voltage-gated outer.membrane
channel
A high-conductance channel was dis-
covered in bilayer voltage-clamp exper-
315