Australian and New Zealand Journal of Obstetrics and Gynaecology 2008; 48: 492– 500 DOI: 10.1111/j.1479-828X.2008.00911.x
492 © 2008 The Authors
Journal compilation © 2008 The Royal Australian and New Zealand College of Obstetricians and Gynaecologists
Blackwell Publishing Asia
Original Article
Combining first and second trimester markers for Down syndrome
screening: Think twice
Robert COCCIOLONE,
1
Kate BRAMELD,
4,5
Peter O’LEARY,
4,6,7
Eric HAAN,
1
Peter MULLER
2
and Karen SHAND
3
1
Department of Genetic Medicine and Department of Paediatrics, University of Adelaide, Adelaide, South Australia,
2
Perinatal Medicine,
Women’s and Children’s Hospital, North Adelaide, South Australia,
3
Ultrasound Specialists for Women, Ashford Specialist Centre, Ashford,
South Australia,
4
Office of Population Health Genomics, Department of Health (WA), Perth, Western Australia,
5
Schools of Population Health
and
6
Women’s and Infants’ Health, University of Western Australia, Crawley, Western Australia, and
7
School of Public Health,
Division of Health Sciences, Curtin University of Technology, Perth, Western Australia, Australia
Aims: This study compares different screening strategies for the detection of Down syndrome and considers practical
implications of using multiple screening protocols.
Methods: The performance characteristics of each screening strategy were assessed based on datasets of Down syndrome
(n = 11) and unaffected pregnancies (n = 1006) tested in both first and second trimester, as well as data from first trimester
(n = 18 901) and second trimester (n = 40 748) pregnancies.
Results: For a detection rate of 91%, the false positive rates for integrated and serum integrated screening were 2.5% and 6.3%,
respectively, compared with combined first trimester (4.6%) and second trimester (12.6%) screening. Contingent and
sequential screening protocols achieved detection rates of 82 to 91% with false positive rates between 2.6 and 2.9%. Contingent
protocols require retesting of 15 to 20% of cases in the second trimester. Sequential and integrated protocols require
retesting of 98 to 100% of cases in the second trimester. The various screening strategies did not always detect the same Down
syndrome pregnancies.
Conclusions: Combining first and second trimester markers for Down syndrome screening better defines the at-risk
population. However, integrated protocols complicate management of screening programs and may not be suitable as primary
screening strategies. It may be a better use of resources to refine current first and second trimester programs through improved
access and new markers. We therefore suggest thinking twice before embracing integrated population screening programs.
Key words: Down syndrome, integrated contingent, first trimester screening.
Introduction
There have been population-based second trimester
antenatal screening programs for Down syndrome and other
fetal anomalies in Australia since 1991.
1
First trimester
combined screening was introduced in 2000 in Australian
and several studies
2–5
have demonstrated first trimester
program performances (detection rate (DR) 83–87% for
a 5% false positive rate (FPR)) comparable with international
groups.
6–8
The majority (78%) of women who undertook
screening tests in Australia in 2004 opted for first
trimester screening.
9
Multiple factors determine which programs women
access. Availability of appropriate ultrasound facilities,
gestational age at presentation, awareness that there is a
choice of screening tests, doctor preference and hospital
guidelines all play a part. Currently Australian policy
guidelines recommend that women should be made aware of
the availability of first and second trimester screening tests
for Down syndrome and other chromosomal abnormalities.
10
However, professional organisations in Canada,
11
the USA
12
and the UK
13
have proposed that women be given a choice
of alternative strategies that include integrated,
14
contingent
15,16
or sequential
17
screening.
The Down syndrome screening protocols reviewed are
outlined in Table 1.
Integrated, contingent and sequential protocols are
based on fetal nuchal translucency (NT) thickness and
maternal serum pregnancy-association plasma protein-A
(PAPP-A) measurements in first trimester and either
triple or quadruple maternal serum markers in the
second trimester.
Integrated screening involves withholding risk odds until
second trimester testing is complete.
7
This approach is
controversial as women do not have the option of early
Correspondence: Mr Robert Cocciolone, Antenatal Screening
(SAMSAS) Program, Genetic Medicine, 72 King William
Road, North Adelaide, SA 5006, Australia.
Email: robert.cocciolone@cywhs.sa.gov.au
Received 14 February 2008; accepted 13 April 2008.