Vol. 64, No. 4, 1997 NEONATAL OVARIAN CYST 557 MI (eds) Pediatric surgery. Year book Medical Publishers, Chicago, 1987; 1341- 1352. 2. Ikeda K, Suita S, Nakano H. Management of ovarian cyst detected antenatally. J Pedi- atr Surg 1988; 23 : 432-435. 3. Wu A, Siegl MJ. Sonography of pelvic masses in children. Am J Radiol 1987; 148 : 1199-1202. 4. Pryse Davies J, Dewhurst CJ : The devel- opment of the ovary and uterus in the fe- tus, newborn and infant : Morphological and enzyme histochemical study. J Pathol 1971; 103 : 5-25. 5. Sakala EP, Leon ZA, Rouse GA. Manage- ment of antenatally diagnosed fetal ovari- an cysts. Obstet-Gynecol-Surv 1991; 46 (7) : 407-414. 6. Von Schweinitz D, Habenicht R, Hayer PF. Spontaneus regression of neonatal ovarian cysts. Monastsschr-Kinderheilkd 1993; 141 (1) :48-52. 7. Hengster P, Menardi G. Ovarian cysts in the newborn. Pediatr Surg Int 1992; 7 : 372- 375. 8. Nussbaum AR, Sanders RC, Hartman DS, Dudegeon DL. Neonatal ovarian cysts :sonographic-pathologic correlation. Pedi- atr Radio 1988; 168 : 817-821. 9. Sapin E, Bargy F, Baron JM. Management of ovarian cysts detected by prenatal ul- trasounds. Eur J Pediatr Surg 1994; 4 (3) : 137-140. 10. Campbell BA, Garg RS, Garg K, Garg V, Otherson HB. Perinatal ovarian cyst : a non-surgical approach. J Pediatr Surg 1992; 27 (12) : 1618-1619. 11. Rodriguez-Balderrama I, Sanches-Carreon EG, Cisneros-Garcia N. A Giant follicular cyst of the ovary in a newborn infant. BoI- Med-Hosp-Infant-Mex 1993; 50 (1) : 53-56. 12. Chao LH, Teng RJ. Congential overian cyst : report of one case. Acta Pediatr Sin 1993; 34 (6) : 480-484. Type Ib Glycogenosis Rita ChristoI)her and K. Taranath Shetty Department of Neurochemistry, National Institute of Mental Health and Neurosciences, Post Box 2900, Bangalore 560 029 Abstract. Type Ib glycogenosis is a rare glycogen storage disorder resulting from a defect in the enzyme, glucose-6-phosphatase microsomal translocase. We report a case of Type Ib glycogenosis in an 18 month-old male child who presented with a history of hypoglycemic seizures and recurrent infections and had a massive hepatomegaly, recurrent hypoglycemia, hyperuricemia, hypertriglyceridemia, neutropenia and fasting lacticacidemia which decreased sharply on glucose administration. (Indian J Pediatr 1997; 64 : 557-560) Key words : Type Ib glycogenosis; Hepatomegaly; Hypoglycemia; Neutropenia. Reprint requests : Dr. Rita Christopher, MD, Assistant Professor, Department of Neurochemistry, NIMHANS, Post Box 2900, Bangalore 560 029. The glycogen storage diseases or glycogenoses are a group of hereditary dis- orders characterised by abnormal concen- tration and/or structure of glycogen in the