https://doi.org/10.1177/0264619617730859
British Journal of Visual Impairment
2018, Vol. 36(1) 5–16
© The Author(s) 2017
Reprints and permissions:
sagepub.co.uk/journalsPermissions.nav
DOI: 10.1177/0264619617730859
journals.sagepub.com/home/jvi
BJVI
Pilot study: Sensory integration
processing disorders in children
with optic nerve hypoplasia
spectrum
Jagjeet Jutley-Neilson
Birmingham City University, UK
Gillian Greville-Harris
University of Birmingham, UK
Jeremy Kirk
Birmingham Children’s Hospital, UK
Abstract
This study aimed to explore the sensory processing profiles of children with the spectrum
of optic nerve hypoplasia (ONH). Caregivers completed the Short Sensory Profile (SSP), the
Social Communication Questionnaire (SCQ), and the Vineland Adaptive Behaviour Scale (VABS)
interview. The study demonstrated that children with ONH present with sensory integration
dysfunction (SID), in their intact senses, and that autistic spectrum condition (ASC) was the best
predictor of SID, rather than visual loss, or level of intellectual disability in these children. The
results indicate that assessment and monitoring of SID in children with ONH is crucial.
Keywords
Optic nerve hypoplasia, sensory integration dysfunction, septo-optic dysplasia, visual impairment
Introduction
Children with the spectrum of optic nerve hypoplasia (ONH) present with variable anatomical
abnormalities and behavioural phenotype, ranging from mild visual loss to total visual loss
(Lambert, Hoyt, & Narahara, 1987), intellectual disability (Garcia-Filion et al., 2008), and autistic
spectrum condition (ASCs) (Jutley-Neilson, Harris, & Kirk, 2013). To date, research reporting
sensory integration dysfunction (SID) (also referred to as sensory processing disorders [SPDs]) in
Corresponding author:
Jagjeet Jutley-Neilson, Division of Psychology, Birmingham City University, 4 Cardigan Street, Birmingham B4 7BD, UK.
Email: jagjeet.jutley-neilson@bcu.ac.uk
730859JVI 0 0 10.1177/0264619617730859British Journal of Visual ImpairmentJutley-Neilson et al.
research-article 2017
Research Article