Gene Section
Short Communication
Atlas Genet Cytogenet Oncol Haematol. 2016; 20(12) 592
Atlas of Genetics and Cytogenetics
in Oncology and Haematology
INIST-CNRS OPEN ACCESS JOURNAL
OCA2 (OCA2 melanosomal transmembrane
protein)
Kunal Ray, Mainak Sengupta, Sampurna Ghosh
Academy of Scientific and Innovative Research (AcSIR), Campus at CSIR - Central Road Research
Institute, Mathura Road, New Delhi - 110 025, kunalray@gmail.com (KR); University of Calcutta,
Department of Genetics, 35, Ballygunge Circular Road, Kolkata - 700 019,
sengupta.mainak@gmail.com); sampurna_ghosh@yahoo.in (MS, SG) India.
Published in Atlas Database: April 2016
Online updated version : http://AtlasGeneticsOncology.org/Genes/OCA2ID45789ch15q12.html
Printable original version : http://documents.irevues.inist.fr/bitstream/handle/2042/66945/04-2016-OCA2ID45789ch15q12.pdf
DOI: 10.4267/2042/66945
This work is licensed under a Creative Commons Attribution-Noncommercial-No Derivative Works 2.0 France Licence.
© 2016 Atlas of Genetics and Cytogenetics in Oncology and Haematology
Abstract
OCA2 gene (OCA2), having a chromosomal
location of 15q12-q13, encodes an integral
membrane transporter protein playing a role in
regulating the pH of melanosomes.
OCA2 is hypothesized to be involved in the transport
of tyrosine, the precursor to melanin synthesis,
within the melanocyte. Defects in this gene are the
cause of oculocutaneous albinism type II; OCA II.
Keywords: OCA2, albinism, OCA II
Identity
Other names: SHEP1, EYCL2, EYCL3, BOCA,
BEY1, BEY2, EYCL, HCL3, PED, BEY, D15S12,
PEDH
HGNC (Hugo): OCA2
Location: 15q12
DNA/RNA
Description
In Chromosome: 15, the 344,486 bases long gene
starts from 27,754,873 bp from pter and ends at
28,099,358 bp from pter; Orientation: Minus strand.
It contains 24 exons and spans ~344.5 kb of the
genome.
Transcription
The gene encodes a 3154 bp transcript.
Alternative splicing results in at least two transcript
variants.
Variant 2 lacks an alternate in-frame exon in the
central coding region, compared to variant 1,
resulting in an isoform that is shorter than isoform 1.
Cytogenetic band showing OCA2 locus (Ref: http://www.genecards.org/cgi-bin/carddisp.pl?gene=OCA2&keywords=OCA2)
Protein