TRENDSin Immunology Vol.22 No.6 June 2001
http://immunology.trends.com 1471-4906/01/$ – see front matter © 2001 Elsevier Science Ltd. All rights reserved. PII: S1471-4906(01)01895-6
285 Research Update Research Update Research Update
Research News
Research on the innate immune response of
mammals has revealed similarities w ith the
invertebrate immune system. Thus, insects
have developed an acute response
resembling that seen in humans,
implicating similar effectors,receptors and
regulation of gene expression. Mussels
have developed intracellular phagocytosis
resembling that seen in mammalian
neutrophils, using cationic antibacterial
peptides in phagolysosomes. Leeches, like
amphibians, contain antibacterial peptides
and immune stimulators that derive from
the processing of neuropeptide precursors.
This pattern of similarities suggests that the
vertebrate innate immune response
resembles a patchwork of those responses
seen in several invertebrate models.
Over more than three billion years,
bacteria have developed a variety of
survival mechanisms that have led to the
appearance of antibiotic-resistant
bacteria
1
. This raises the question: how are
bacteria kept in check by multicellular
organisms? Research on the immune
systems of invertebrates, such as insects,
has shown that they have developed a
battery of natural antibacterial peptides,
such as defensin and cecropins
2,3
, as part of
their innate response to bacteria. In
addition, antibacterial peptides have been
identified in the glandular cells of
amphibian skin (e.g. magainins,
dermaseptins and ranalexin), humans
(e.g. defensins, hadrurin and hepcidin) and
plants [e.g. thionins, snaking-1 and
antifungal peptides from seeds of
Phytolacca americana (PAFP-s)],
reflecting the universal nature of such
natural defense mechanisms
4–9
. However,
although these antibacterial peptides are
present throughout the living kingdom, it
is interesting to see how they have evolved.
Human antimicrobial responses
In humans, some antimicrobial peptides
are produced by the epithelial cells that
line the respiratory, gastrointestinal and
urogenital tracts and the skin
9
. Epithelial
granulocytes of the small intestine
contribute to the barrier function of the
gastric mucosa by the apical release of
granules containing a variety of
antimicrobial products, including human
α-defensin-5 and -6 (Ref. 5). Other similar
peptides are found in the glandular
secretions that moisten and lubricate
such surfaces
2
. Others, such as
human β-defensins, are abundant in
certain migratory phagocytic cells
that can surround, ingest and kill
microbial invaders
9
.
Invertebrate immune responses
Insects, such as Drosophila, respond to
septic injuries by rapidly synthesizing
antimicrobial peptides (Fig. 1). These
peptides are predominantly produced in
the fat body; they are then secreted into the
hemolymph and participate in a systemic
response
10
. Seven distinct antimicrobial
peptides (plus isoforms) have been
described for Drosophila. Interestingly,
they appear to have distinct target
specificities, and induction of the
expression of the various peptides depends
on the type of infectious agent. Fungal
infection, for example, results in a strong
induction of the antifungal peptide
drosomycin, whereas the antibacterial
peptides drosocin and diptericin are only
weakly induced
11
. Conversely, challenge
with Gram-negative bacteria strongly
induces the antibacterial peptide genes,
but has a less marked effect on drosomycin
expression
11
. Drosophila can discriminate
between various groups of microorganisms
and mount a somewhat adaptive immune
response
12
. The gene Spaetzle codes for a
secreted protein of the cysteine-knot family
of growth factors, which is activated by
proteolytic cleavage
12
. The processed
Spaetzle product is thought to bind to and
activate the transmembrane receptor Toll,
although direct interaction between the
two proteins has not been reported to date.
Toll activation is transduced through the
adapter molecule Tube and the
serine/threonine kinase Pelle, and leads to
the phosphorylation and subsequent
degradation of the inhibitor Cactus
12
.
Cactus degradation frees Dif (a member of
the Rel family of transcription factors),
which translocates to the nucleus, where it
is thought to bind to and activate the
Drosomycin promoter
13
. The same genetic
analysis revealed that expression of the
antibacterial peptides drosocin and
diptericin is independent of Toll
12
. The
discovery of the key role played by Toll in
the Drosophila host defense led to the
description of the first mammalian Toll
homolog, now referred to as the Toll-like
receptor 4 (TLR4). Two such homologs,
TLR2 and TLR4, were shown to play
crucial roles in vertebrate innate immunity
against bacteria
13
. TLR2 was shown to play
a parallel role in response to peptidoglycan
derived from the Gram-positive bacterial
cell wall
12
. Eight additional Toll-related
genes (Toll, Toll-3–Toll-8, as well as
18-wheeler), are present in the Drosophila
genome. Two of these genes, Toll-3 and
Toll-4, are expressed at low levels; by
contrast, Toll-6, -7 and -8 are expressed at
high levels during embryogenesis and
molting, suggesting that Toll and 18w are
involved in development
13
. As well as the
Toll pathway, two other pathways more
specific for bacterial infection have been
demonstrated in Drosophila, namely, imd
and 18w (Fig. 1), reflecting the diversity
and specificity of responses to pathogens in
insects.
Epithelial immune responses
Recent studies on antimicrobial peptides
from Drosophila have shown that a variety
of epithelial tissues in direct contact with
the external environment can express the
antifungal Drosophila peptide drosomycin,
suggesting that a local response to
infections is affecting these barrier
tissues
12
. The imd gene in Drosophila plays
a crucial role in the activation of this local
response to infection. Drosomycin
expression is regulated by the Toll pathway
during the systemic response, but is
regulated by imd in the respiratory tract,
thus demonstrating the existence of distinct
regulatory mechanisms for local and
systemic induction of antimicrobial peptide
Vertebrate innate immunity resembles a mosaic of
invertebrate immune responses
Michel Salzet