Journal of Neurorhenii.strv
I .ippincoit—Ravcn Publishers, Philadelphia
© 1996 International Society for Neurochemistry
Kynurenine Disposition in Blood and Brain of Mice:
Effects of Selective Inhibitors of Kynurenine
Hydroxylase and of Kynureninase
Alberto Chiarugi, Raffaella Carpenedo, and Flavio Moroni
Department o~ /‘reclinical and Clinical Pharmacology, University of Florence, Florence, Italy
Abstract: To study the regulation of the synthesis of quin-
olinic and kynurenic acids in vivo, we evaluated (a) the
metabolism of administered kynurenine by measuring the
content of its main metabolites 3-hydroxykynurenine, an-
thranilic acid, and 3-hydroxyanthranilic acid in blood and
brain of mice; (b) the effects of (m-nitrobenzoyl)alanine,
a selective inhibitor of kynurenine hydroxylase and of (o-
methoxybenzoyl)alanine, a selective inhibitor of kynureni-
nase, on this metabolism; and (c) the effects of (a-me-
thoxybenzoyl)alanine on liver kynureninase and 3-hydro-
xykynureninase activity. The conclusions drawn from
these experiments are (a) the disposition of administered
kynurenine preferentially occurs through hydroxylation in
brain and through hydrolysis in peripheral tissues; (b) (m-
nitrobenzoyl)alanine, the inhibitor of kynurenine hydroxy-
lase, causes the expected changes in brain kynurenine
metabolism, such as a decrease of 3-hydroxykynurenine,
and an increase of kynurenic acid; and (c) (o-methoxy-
benzoyl) alanine, the kynureninase inhibitor, increases
brain concentration of the cytotoxic compound 3-hydra-
xykynurenine, and unexpectedly does not reduce brain
concentration of 3-hydroxyanthranilic acid, the direct pre-
cursor of quinolinic acid. Taken together, the experiments
suggest that the systemic administration of a kynurenine
hydroxylase inhibitor is a rational approach to increase
the brain content of kynurenate and to decrease that of
cytotoxic kynurenine metabolites, such as 3-hydroxyky-
nurenine and quinolinic acid. Key Words: Quinolinic
acid— Kynurenic acid— NMDA— Kynurenine— Kynuren-
ne hydroxylase— Kynureninase.
J. Neurochem. 67, 692—698 (1996).
The opening of the indole ring of tryptophan occurs
as a consequence of the action of the enzymes trypto-
phan 2,3-dioxygenase (EC 1.13.1.2), which is located
mainly in the liver but is also present in brain (Haber
et al., 1993), and indoleamine 2,3-dioxygenase (EC
1.13.11.17), which has been identified in a number
of extrahepatic tissues, including brain (Yoshida and
Hayashi, 1987). This opening is the rate-limiting step
pathway for the formation of a group of compounds
collectively named “kynurenines” (Fig. I). At least
two kynurenines, kynurenic acid (KYNA) and quino-
linic acid (QUIN), are able to interact with the excit-
atory amino acid receptors (Stone and Perkins, 1981:
Perkins and Stone, 1982). KYNA is a noncompetitlve
antagonist of the N-rnethyl-D-aspartate (NMDA) re-
ceptor ion channel complex, acting on the strychnine-
insensitive glycinc recognition site (Johnson and
Ascher, 1987) with an 1C
5() value in the low micromo-
lar range (Kessler et al., 1989; Pellegrini-Giampictro
et al., 1989). At higher concentrations, it is also able
to interact, as a competitive antagonist, on AMPA and
kainate receptors (Stone, 1993). On the contrary.
QUIN exerts opposite effects, acting as an NMDA
receptor agonist able to cause excitotoxic lesions
(Schwarcz et al., 1983). Another kynurenine metabo-
lite, picolinic acid, has been shown recently to he an
activator of macrophage function (Varesio et al., 1990)
and, finally, 3-hydroxykynurenine (30H-.kynurenine)
has been shown to possess cytotoxic effects in a neu-
ronal cell line (Eastman and Guilarte, 1989).
Excessive stimulation of the ionotropic glutamate
receptors has been observed in a number of neurologi-
cal diseases such as epilepsy, stroke, and several de-
generative disorders (Meldrum and Garthwaite, 1990:
Rogawski, 1992). Furthermore, changes in the concen-
tration of toxic kynurenines have been demonstrated in
the course of infections involving the central nervous
system (Heyes et al., 1991 ) and in models of multiple
sclerosis (Flanagan et al., 1995). In view of the possi-
ble importance of kynurenine metabolites in such a
large variety of central nervous system pathologies,
we previously investigated the effects of several inhibi-
tors of the enzymes involved in kynurenine metabolism
in rodents. Such inhibitors were tested in an attenipt
Received November 6, 1995; revised manuscript received March
12, 1996; accepted March 19, 1996.
Address correspondence and reprint requests to Dr. F. Moroni al
Dipartimento di Farmacologia Preclinica e Clinica, Università di
Firenze, Viale Morgagni 65, 50124 Firenze, Italy.
Abbreviations used: KYNA, kynurenic acid; NMDA, N-methyl-
D-aspartate; mNBA, (mn-nitrohenzoyl) alaninc; oMBA, (o-rnethoxy-
benzoyl )alanine; 30H-kynurenine, 3-hydroxykynurenine; 30H-an-
thranilic acid, 3-hydroxyanthranilic acid; QUIN, quinolinic acid.
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