© 1999 Macmillan Magazines Ltd
sible for the accumulation of dendritic cells
in the lymph nodes of type II — but not type
I — ALPS patients
2
. Wang et al. showed that
killing of dendritic cells by CD4-positive T
cells is mediated mainly by the tumour-
necrosis factor-related apoptosis-inducing
ligand (TRAIL), through its receptor DR5,
instead of by the Fas–FasL interaction. But
dendritic cells from patients with type II
ALPS are resistant to such TRAIL-mediated
apoptosis. Using retroviral transduction, the
authors further showed that mutant cas-
pase-10 could interfere with TRAIL-mediat-
ed apoptosis in normal dendritic cells.
Wang et al. have documented, for the first
time, caspase mutations in a human disease.
Although their study clearly shows that peo-
ple with type II ALPS carry mutant forms of
caspase-10 that can interfere with apoptotic
pathways of many death receptors, it raises
other issues. First, it has yet to be established
conclusively that mutation in caspase-10 is
solely responsible for the ALPS in these
patients. Are the expression levels of FADD
and caspase-8 normal? And, despite the
evidence that mutations in caspase-10 are
responsible for the defective apoptosis in
dendritic cells, the normal expression and
function of TRAIL receptors in the patients
should be measured.
Second, the dominant effect of the het-
erozygous caspase-10 mutant remains
intriguing. Although the most likely possi-
bility is that this mutant interferes with com-
plex formation by directly binding to cas-
pase-8 and FADD, such a picture does not
explain why patients carrying the heterozy-
gous allele have few clinical manifestations.
This difference has also been noticed among
type I ALPS patients with heterozygous
mutations in Fas, and it probably reflects the
presence of other genetic modifying ele-
ments. In the lpr mouse model, for example,
the animals show varied symptoms with
different genetic backgrounds
11
.
Finally, the defective apoptosis of den-
dritic cells in patients with type II ALPS is a
significant finding. The sustained lifespan of
mature dendritic cells presenting self anti-
gens could lead to enhanced autoreactivity
of lymphocytes
12
. So, the involvement of
TRAIL — and, as revealed here, possibly cas-
pase-10 — in mediating dendritic cell death
might provide new avenues for studying the
regulation of dendritic cell lifespan, and its
possible role in causing autoimmunity
13
.
Five years after caspase-1 was shown to be
the mammalian homologue of the nematode
death protein ced-3, more than a dozen cas-
pases have been identified
3
. Knockout studies
have produced surprises about the involve-
ment of caspases in mammalian develop-
ment
14
. This latest finding by Wang and col-
leagues underscores the fact that caspases are
indispensable in mammalian apoptosis, and
further establishes these proteases as potential
therapeutic targets for clinical applications.
Timothy S. Zheng is at Biogen Inc., 14 Cambridge
Center, Cambridge, Massachusetts 02142, USA.
e-mail: timothy.zheng@biogen.com
Richard A. Flavell is in the Section of
Immmunobiology, Yale University School of
Medicine, and the Howard Hughes Medical
Institute, 310 Cedar Street, New Haven,
Connecticut 06510, USA.
e-mail: fran.manzo@yale.edu
1. Abbas, A. K. Cell 84, 655–657 (1996).
news and views
NATURE | VOL 400 | 29 JULY 1999 | www.nature.com 411
Science policy
The business of research
Henk F. Moed and Marc Luwel
O
n page 433 of this issue, Plerou et
al.
1
provide a quantitative study of
the academic research system. Such
studies are essential in examining claims as
to the success (or otherwise) of the system in
general, and forms of funding in particular.
Whether the claims come from university
scientists or policy makers, anecdote is no
substitute for data.
The authors find that the growth dynam-
ics of universities in the United States resem-
ble those of business companies. In the same
way that market forces operate in business,
the peer review system appears to keep com-
petition among scientists sufficiently strong.
This intriguing result may mean that there is
no need to make academic research at uni-
versities more business-like than it is already.
Plerou et al. include five different mea-
sures of research activity in their analysis.
The largest database consists of 17 years of
annual research and development (R&D)
expenditure in science and engineering for
719 US universities. The authors find that the
growth in research activity does not depend
on the size of R&D expenditure (that is, the
size of the university), in the same way that
businesses (whether large or small) are sub-
ject to universal growth mechanisms. They
find the same pattern in their analysis of the
number of papers and patents published by
more than 100 US universities over a similar
time period. Moreover, they see the same
behaviour in growth rates for research fund-
ing in English and Canadian universities,
suggesting that the broad result holds for
different academic systems.
Some historical context may help here.
The classical von Humboldt model of uni-
versities — carrying out pure research with-
out any consideration of practical applica-
tion — was characterized by learning
through science, and the unity of research
and teaching
2
; conducting pure research was
assumed to be the most appropriate training
for a job in society. After the Second World
War, this system underwent gradual trans-
formation. The concept of pure research was
increasingly replaced by one of fundamental
research; intended to advance our knowl-
edge of nature, but often motivated by and
funded for specific technological objectives.
Besides their traditional mission of pro-
viding academic training and carrying out
fundamental research, universities today are
expected to help solve society’s problems and
strengthen economic development. In con-
sequence, a new mode of knowledge produc-
tion
3
has arisen, involving interdisciplinary
research with the aim of applying knowledge
in more rapid and flexible ways. These trends
raise the question as to whether universities
can continue to contribute to long-term
basic research and maintain a balance
between training and knowledge production
and application
4
.
Plerou and colleagues are rather cautious
in drawing general conclusions from their
findings. They note that some may see the
business sector as a model for academic
research. In these terms, the academic
research system may be considered effective,
and one could conclude that the funding
structure of research in the United States,
particularly the relatively high proportion of
short-term research grants, should be a
model for other countries. On the other
hand, the authors suggest that the similarity
in the growth dynamics of research and busi-
ness output may show that the ‘economiza-
tion’ of fundamental research has been
pushed too far in some Western countries. A
key factor here is that the ‘time horizon’ (the
number of years that management looks
ahead) in the business sector is now typically
five years or less, whereas in fundamental
research it is often believed to be much
longer
5
. In this context, the findings of Plerou
et al.
1
reflect a convergence of the time hori-
zons of business and universities. To make
fundamental contributions to science, the
research programmes of high-quality groups
have to continue for more than five years —
longer than the average research grant.
What drawbacks and limitations are
there to Plerou and colleagues’ analysis?
Their approach aims to characterize the
system as a whole. As a result, deviations
from the general pattern are not discussed,
although such differences may help show
2. Wang, J. et al. Cell 98, 47–58 (1999).
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5. Canale, V. & Smith, C. J. Pediatr. 70, 891–899 (1967).
6. Nagata, S. J. Hum. Genet. 43, 2–8 (1998).
7. Straus, S. E. et al. Ann. Intern. Med. 130, 591–601(1999).
8. Ashkenzi, A. & Dixit, V. M. Science 281, 1305–1308 (1998).
9. Dianzani, U. et al. Blood 89, 2871–2879 (1997).
10. Sneller, M. C. et al. Blood 89, 1341–1348 (1997).
11. Steinberg, A. D. Semin. Immunol. 6, 55–69 (1994).
12. Ludewig, B. et al. J. Exp. Med. 188, 1493–1501 (1998).
13.Banchereau, J. & Steinman, R. M. Nature 392, 245–252 (1998).
14.Zheng, T. S. et al. Cell Death Differ. (in the press).